Zobrazeno 1 - 10
of 35
pro vyhledávání: '"François Van Hoof"'
Autor:
Jean-Louis Habib Jiwan, André Schanck, R. Libert, Georges Laus, François Van Hoof, Philippe De Nayer, Edmond de Hoffmann
Publikováno v:
Clinica Chimica Acta. 355:145-151
Ethylsuccinylcarnitine, a previously undescribed acylcarnitine, was identified in urines obtained from 81% of adult volunteers. Its chemical structure was obtained by 1H nuclear magnetic resonance spectroscopy of the urinary purified compound and con
Autor:
François Van Hoof, André Schanck, Edmond de Hoffmann, R. Libert, Marc Thillaye, Marie-Cécile Nassogne, Marie-Françoise Vincent
Publikováno v:
Clinica Chimica Acta. 295:87-96
In urine of patients with propionyl-CoA carboxylase deficiency or with methylmalonic acidemia, carnitine esters of 2-methyl-branched fatty acids of all chain lengths between 4 and 9 atoms of carbon were identified during the acute phase of the diseas
Publikováno v:
Environmental Toxicology and Chemistry. 15:1317-1323
The Musselmonitor® (Delta Consult, Kapelle, The Netherlands) is a biomonitor that uses the valve position and the activity of eight Dreissena polymorpha to monitor the water quality. The normal behavior was studied to evaluate whether eight mussels
Autor:
Jean-Paul Buts, François Van Hoof, Pierre Rustin, Isabel Goncalves, Arnold Munnich, Jean de Ville de Goyet, Raymond Reding, Jean-Bernard Otte, Dominique Chretien, Etienne Sokal, Dominique Hermans, Jean-Marie Saudubray
Publikováno v:
Journal of Hepatology. 23:290-294
Two siblings presented with neonatal cholestasis and early liver insufficiency. The older was admitted for end-stage cirrhosis with severe hypoglycemia and had long-term successful liver transplant at the age of 15 months. The second child presented
Publikováno v:
Journal of the American Society for Mass Spectrometry. 6:588-596
Fragmentation of negative ions produced by fast-atom bombardment (FAB) from 14 tauroconjugated bile acids and some of their deuterated analogs has been studied by mass spectrometry and by collision-induced dissociation (CID) tandem mass spectrometry
Publikováno v:
Water Science and Technology. 30:79-86
A biological early warning system based on the phototactic behaviour of Daphnia magna has been evaluated in relation to the reproducibility of its response and sensitivity towards potential pollutants. In addition to the infrared detection system of
Publikováno v:
Biochemical Pharmacology. 43:2435-2442
The inhibitory effects of valproate (VPA) and nine of its metabolites on mitochondrial oxidations have been investigated. Valproate, 4-ene-VPE, 2,4-diene-VPA and 2-propylglutaric acid inhibited the rate of oxygen consumption by rat liver mitochondria
Publikováno v:
Biochemical Pharmacology. 41:1419-1428
Chronic administration to rats of the anticonvulsant drug, valproate, induced proliferation of liver peroxisomes and selectively increased the activity of the enzymes involved in beta-oxidation in these organelles. In kidney cortex, only a moderate i
Autor:
François, Van Hoof, Peter, Van Wiele, Franvoise, Acobas, Jean-Luc, Guinamant, Auguste, Bruchet, Isabelle, Schmitz, Ivana, Bobeldijk, Frank, Sacher, Francesc, Ventura, Rosa, Boleda
Publikováno v:
Journal of AOAC International. 85(2)
As part of a project funded by the European Commission (EC) for the development and evaluation of multiresidue methods for analysis of drinking and related waters, 17 European laboratories evaluated a method using styrene-divinylbenzene copolymer sol
Autor:
Lucien Koulischer, François Van Hoof, Alain Verloes, Jacques Rigo, Bettina Grattagliano, Martial M. Massin, Jacques Lombet, Soyeur D
Publikováno v:
American journal of medical genetics. 72(2)
We describe a boy with an early lethal hypertrophic vacuolar cardiomyopathy of neonatal onset. Abnormal intra-and extralysosomal glycogen storage disease was demonstrated in heart and skeletal muscles. Glycogen content was twice the normal in muscles