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Autor:
Erica Del Giudice, Norma Decaminada, M. Mortilla, Désirée Caselli, Maria Cappellini, Claudio Fonda, Maurizio Aricò, Elena Sieni
Publikováno v:
Child's Nervous System. 26:121-127
Familial hemophagocytic lymphohistiocytosis (FHL) is a rare multisystem congenital disorder characterized by uncontrolled proliferation and infiltration of activated lymphocytes and histiocytes, secreting high amounts of inflammatory cytokines; this