Zobrazeno 1 - 10
of 54
pro vyhledávání: '"Enrica Federti"'
Autor:
Alessandro Mattè, Enrica Federti, Antonio Recchiuti, Moayed Hamza, Giulia Ferri, Veronica Riccardi, Jacopo Ceolan, Alice Passarini, Filippo Mazzi, Angela Siciliano, Deepak L Bhatt, David Coughlan, John Climax, Elisa Gremese, Carlo Brugnara, Lucia De Franceschi
Publikováno v:
Haematologica, Vol 109, Iss 6 (2023)
Inflammatory vasculopathy is critical in sickle cell disease (SCD)-associated organ damage. An imbalance between pro-inflammatory and pro-resolving mechanisms in response to different triggers such as hypoxia/reoxygenation or infections has been prop
Externí odkaz:
https://doaj.org/article/4fbd0b212afd45d98532086bb0bd5574
Autor:
Serge Cedrick Toya Mbiandjeu, Angela Siciliano, Alessandro Mattè, Enrica Federti, Massimiliano Perduca, Davide Melisi, Immacolata Andolfo, Angela Amoresano, Achille Iolascon, Maria Teresa Valenti, Francesco Turrini, Michele Bovi, Arianna Pisani, Antonio Recchiuti, Domenico Mattoscio, Veronica Riccardi, Luca Dalle Carbonare, Carlo Brugnara, Narla Mohandas, Lucia De Franceschi
Publikováno v:
Antioxidants, Vol 13, Iss 4, p 454 (2024)
Aging is characterized by increased oxidation and reduced efficiency of cytoprotective mechanisms. Nuclear factor erythroid-2-related factor (Nrf2) is a key transcription factor, controlling the expression of multiple antioxidant proteins. Here, we s
Externí odkaz:
https://doaj.org/article/6113bcf2028948f886726cd52fe80fab
Autor:
Alessandro Matte, Anand B. Wilson, Federica Gevi, Enrica Federti, Antonio Recchiuti, Giulia Ferri, Anna Maria Brunati, Mario Angelo Pagano, Roberta Russo, Christophe Leboeuf, Anne Janin, Anna Maria Timperio, Achille Iolascon, Elisa Gremese, Lenny Dang, Narla Mohandas, Carlo Brugnara, Lucia De Franceschi
Publikováno v:
JCI Insight, Vol 8, Iss 20 (2023)
Hereditary spherocytosis (HS) is the most common, nonimmune, hereditary, chronic hemolytic anemia after hemoglobinopathies. The genetic defects in membrane function causing HS lead to perturbation of the RBC metabolome, with altered glycolysis. In mi
Externí odkaz:
https://doaj.org/article/dca369d1197d4e2db25239462d156007
Autor:
Enrica Federti, Alessandro Matte, Antonio Recchiuti, Francesca Garello, Alessandra Ghigo, Wassim El Nemer, Enzo Terreno, Angela Amoresano, Domenico Mattoscio, Franco Turrini, Christophe Lebouef, Anne Janin, Antonella Pantaleo, Roberta Russo, Mickael Marin, Iana Iatcencko, Veronica Riccardi, Angela Siciliano, Achille Iolascon, Carlo Brugnara, Lucia De Franceschi
Publikováno v:
HemaSphere, Vol 7, Iss 3, p e848 (2023)
Drug repurposing is a valuable strategy for rare diseases. Sickle cell disease (SCD) is a rare hereditary hemolytic anemia accompanied by acute and chronic painful episodes, most often in the context of vaso-occlusive crisis (VOC). Although progress
Externí odkaz:
https://doaj.org/article/c8c05eebb53a44d484b867d2b88dc0d7
Autor:
Alessandro Mattè, Penelope A. Kosinski, Enrica Federti, Lenny Dang, Antonio Recchiuti, Roberta Russo, Angela Siciliano, Veronica Riccardi, Anne Janin, Matteo Mucci, Christophe Leboeuf, Achille Iolascon, Carlo Brugnara, Lucia De Franceschi
Publikováno v:
Haematologica, Vol 108, Iss 9 (2023)
Externí odkaz:
https://doaj.org/article/29ab57f703ca467ca865adac1fdc12ac
Autor:
Enrica Federti, Francesca Vinchi, Iana Iatcenko, Alessandra Ghigo, Alessandro Matte, Serge Cedrick Mbiandjeu Toya, Angela Siciliano, Deborah Chiabrando, Emanuela Tolosano, Steven Zebulon Vance, Veronica Riccardi, Immacolata Andolfo, Manuela Iezzi, Alessia Lamolinara, Achille Iolascon, Lucia De Franceschi
Publikováno v:
Haematologica, Vol 108, Iss 5 (2023)
Cardiomyopathy deeply affects quality of life and mortality of patients with b-thalassemia or with transfusion-dependent myelodysplastic syndromes. Recently, a link between Nrf2 activity and iron metabolism has been reported in liver ironoverload mur
Externí odkaz:
https://doaj.org/article/d770bb7369b841549626d8fc27416aca
Autor:
Kevin Peikert, Enrica Federti, Alessandro Matte, Gabriela Constantin, Enrica Caterina Pietronigro, Paolo Francesco Fabene, Paola Defilippi, Emilia Turco, Federico Del Gallo, Pietro Pucci, Angela Amoresano, Anna Illiano, Flora Cozzolino, Maria Monti, Francesca Garello, Enzo Terreno, Seth Leo Alper, Hannes Glaß, Lisann Pelzl, Katja Akgün, Tjalf Ziemssen, Rainer Ordemann, Florian Lang, Anna Maria Brunati, Elena Tibaldi, Immacolata Andolfo, Achille Iolascon, Giuseppe Bertini, Mario Buffelli, Carlo Zancanaro, Erika Lorenzetto, Angela Siciliano, Massimiliano Bonifacio, Adrian Danek, Ruth Helen Walker, Andreas Hermann, Lucia De Franceschi
Publikováno v:
Acta Neuropathologica Communications, Vol 9, Iss 1, Pp 1-15 (2021)
Abstract Chorea-Acanthocytosis (ChAc) is a devastating, little understood, and currently untreatable neurodegenerative disease caused by VPS13A mutations. Based on our recent demonstration that accumulation of activated Lyn tyrosine kinase is a key p
Externí odkaz:
https://doaj.org/article/41fdfcd9d3254dc9b0d9bd47117287f7
Autor:
Paolo Rossato, Enrica Federti, Alessandro Matte, Helmut Glantschnig, Fabio Canneva, Maria Schuster, Sogue Coulibaly, Gerald Schrenk, Dirk Voelkel, Michael Dockal, Barbara Plaimauer, Immacolata Andolfo, Achille Iolascon, Hanspeter Rottensteiner, Herbert Gritsch, Friedrich Scheiflinger, Werner Hoellriegl, Lucia De Franceschi
Publikováno v:
Haematologica, Vol 107, Iss 11 (2022)
Sickle cell disease (SCD) is an inherited red blood cell disorder that occurs worldwide. Acute vaso-occlusive crisis is the main cause of hospitalization in patients with SCD. There is growing evidence that inflammatory vasculopathy plays a key role
Externí odkaz:
https://doaj.org/article/8c70e0b3cd1f416b96b51f9736f32503
Autor:
Enrica Federti, Alessandro Matte, Veronica Riccardi, Kevin Peikert, Seth L. Alper, Adrian Danek, Ruth H. Walker, Angela Siciliano, Iana Iatcenko, Andreas Hermann, Lucia De Franceschi
Publikováno v:
Antioxidants, Vol 11, Iss 1, p 76 (2021)
The peroxiredoxins (PRXs) constitute a ubiquitous antioxidant. Growing evidence in neurodegenerative disorders such as Parkinson’s disease (PD) or Alzheimer’s disease (AD) has highlighted a crucial role for PRXs against neuro-oxidation. Chorea-ac
Externí odkaz:
https://doaj.org/article/01dd47480869426cad9fafbd3dbf3ae6
Autor:
Enrica Federti, Alessandro Matte, Alessandra Ghigo, Immacolata Andolfo, Cimino James, Angela Siciliano, Christophe Leboeuf, Anne Janin, Francesco Manna, Soo Young Choi, Achille Iolascon, Elisabetta Beneduce, Davide Melisi, Dae Won Kim, Sonia Levi, Lucia De Franceschi
Publikováno v:
Data in Brief, Vol 15, Iss , Pp 376-381 (2017)
The data presented in this article are related to the research paper entitled âperoxiredoxin-2 plays a pivotal role as multimodal cytoprotector in the early phase of pulmonary hypertensionâ (Federti et al., 2017) [1]. Data show that the absence of
Externí odkaz:
https://doaj.org/article/e1a07604cb984fb3b6cfe6da54356ce2