Zobrazeno 1 - 10
of 19
pro vyhledávání: '"Emilia Baranowska"'
Autor:
Chiranjit Panja, Katarzyna Niedzwiecka, Emilia Baranowska, Jaroslaw Poznanski, Roza Kucharczyk
Publikováno v:
Scientific Reports, Vol 13, Iss 1, Pp 1-13 (2023)
Abstract Defects in ATP synthase functioning due to the substitutions in its two mitochondrially encoded subunits a and 8 lead to untreatable mitochondrial diseases. Defining the character of variants in genes encoding these subunits is challenging d
Externí odkaz:
https://doaj.org/article/3aa022f26e704d0aaf5a4132ea80e411
Publikováno v:
Scientific Reports, Vol 13, Iss 1, Pp 1-18 (2023)
Abstract The mitochondrial ATP synthase, an enzyme that synthesizes ATP and is involved in the formation of the mitochondrial mega-channel and permeability transition, is a multi-subunit complex. In S. cerevisiae, the uncharacterized protein Mco10 wa
Externí odkaz:
https://doaj.org/article/0404c5843dfc4e2793f103c408a4e941
Autor:
Emilia Baranowska, Katarzyna Niedzwiecka, Chiranjit Panja, Camille Charles, Alain Dautant, Jarosław Poznanski, Jean-Paul di Rago, Déborah Tribouillard-Tanvier, Roza Kucharczyk
Publikováno v:
Disease Models & Mechanisms, Vol 16, Iss 4 (2023)
Externí odkaz:
https://doaj.org/article/67af0f6874f24f29be4f95b9a79d1e6c
Publikováno v:
Cellular Physiology and Biochemistry, Vol 54, Iss 2, Pp 211-229 (2020)
Externí odkaz:
https://doaj.org/article/b06111c019de491b91d9e752de1f7e7e
Autor:
Gaétan Bader, Ludovic Enkler, Yuhei Araiso, Marine Hemmerle, Krystyna Binko, Emilia Baranowska, Johan-Owen De Craene, Julie Ruer-Laventie, Jean Pieters, Déborah Tribouillard-Tanvier, Bruno Senger, Jean-Paul di Rago, Sylvie Friant, Roza Kucharczyk, Hubert Dominique Becker
Publikováno v:
eLife, Vol 9 (2020)
A single nuclear gene can be translated into a dual localized protein that distributes between the cytosol and mitochondria. Accumulating evidences show that mitoproteomes contain lots of these dual localized proteins termed echoforms. Unraveling the
Externí odkaz:
https://doaj.org/article/445f392680da4554b57ee4bf06f5d463
Autor:
Emilia Baranowska, Katarzyna Niedzwiecka, Chiranjit Panja, Camille Charles, Alain Dautant, Jean-Paul di Rago, Déborah Tribouillard-Tanvier, Roza Kucharczyk
Publikováno v:
Human Molecular Genetics. 32:1313-1323
The mitochondrial DNA mutation m.9032T>C was previously identified in patients presenting with NARP (Neuropathy Ataxia Retinitis Pigmentosa). Their clinical features had a maternal transmission and patient’s cells showed a reduced oxidative phospho
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::30a3ce86f3b93e53327ea230ac2dac38
https://doi.org/10.1093/hmg/ddac292
https://doi.org/10.1093/hmg/ddac292
In S. cerevisiae, the uncharacterized protein Mco10 (Mitochondrial class one protein of 10 kDa) was previously found to be associated with mitochondrial ATP synthase and referred to as a new ‘subunit l’. However, recent cryo-EM structures of S. c
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::556b25e63cbe1d5c4ea3ab18c82508e9
https://doi.org/10.1101/2022.07.02.498517
https://doi.org/10.1101/2022.07.02.498517
Autor:
Anna M Kabala, Krystyna Binko, François Godard, Camille Charles, Alain Dautant, Emilia Baranowska, Natalia Skoczen, Kewin Gombeau, Marine Bouhier, Hubert D Becker, Sharon H Ackerman, Lars M Steinmetz, Déborah Tribouillard-Tanvier, Roza Kucharczyk, Jean-Paul di Rago
Publikováno v:
Genetics. 220
The yeast mitochondrial ATP synthase is an assembly of 28 subunits of 17 types of which 3 (subunits 6, 8, and 9) are encoded by mitochondrial genes, while the 14 others have a nuclear genetic origin. Within the membrane domain (FO) of this enzyme, th
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::68434d49f0ca16e1dbad40619ae05fc8
https://doi.org/10.1093/genetics/iyac007
https://doi.org/10.1093/genetics/iyac007
Autor:
Gaetan Bader, Ludovic Enkler, Yuhei Araiso, Marine Hemmerle, Krystyna Bińko, Emilia Baranowska, Aneta Więsyk, Johan-Owen De Craene, Julie Ruer-Laventie, Jean Pieters, Deborah Tribouillard-Tanvier, Bruno Senger, Jean-Paul di Rago, Sylvie Friant, Hubert Dominique Becker, Róża Kucharczyk
Publikováno v:
Biochimica et Biophysica Acta (BBA) - Bioenergetics. 1863:148895
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::d93d0e213b8ea078c9940040d7fb4320
https://doi.org/10.1016/j.bbabio.2022.148895
https://doi.org/10.1016/j.bbabio.2022.148895
Autor:
Anna Kabala, Krystyna Binko, Francois Godard, Alain Dautant, Emilia Baranowska, Natalia Skoczen, Kevin Gombeau, Marine Bouhier, Hubert Becker, Sharon Ackerman, Lars Steinmetz, Deborah Tribouillard-Tanvier, Roza Kucharczyk, Jean-Paul di Rago
Publikováno v:
Biochimica et Biophysica Acta (BBA) - Bioenergetics. 1863:148786
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::daa496b86c2c1a93b84f0187584b5da9
https://doi.org/10.1016/j.bbabio.2022.148786
https://doi.org/10.1016/j.bbabio.2022.148786