An adjudication algorithm for respiratory-related hospitalisation in idiopathic pulmonary fibrosis

Autor: Paul Ford, Michael Kreuter, Kevin K. Brown, Wim A. Wuyts, Marlies Wijsenbeek, Dominique Israël-Biet, Richard Hubbard, Steven D. Nathan, Hilario Nunes, Bjorn Penninckx, Niyati Prasad, Ineke Seghers, Paolo Spagnolo, Nadia Verbruggen, Nik Hirani, Juergen Behr, Robert J. Kaner, Toby M. Maher

Publikováno v: ERJ Open Research, Vol 10, Iss 1 (2024)

Background There is no standard definition of respiratory-related hospitalisation, a common end-point in idiopathic pulmonary fibrosis (IPF) clinical trials. As diverse aetiologies and complicating comorbidities can present similarly, external adjudi

Externí odkaz: https://doaj.org/article/dd10a57961ca4f14aca9968ef542372a

In smokers, Sonic hedgehog modulates pulmonary endothelial function through vascular endothelial growth factor

Autor: Priscilla Henno, Stanislas Grassin-Delyle, Emeline Belle, Marion Brollo, Emmanuel Naline, Edouard Sage, Philippe Devillier, Dominique Israël-Biet

Publikováno v: Respiratory Research, Vol 18, Iss 1, Pp 1-8 (2017)

Abstract Background Tobacco-induced pulmonary vascular disease is partly driven by endothelial dysfunction. The Sonic hedgehog (SHH) pathway is involved in vascular physiology. We sought to establish whether the SHH pathway has a role in pulmonary en

Externí odkaz: https://doaj.org/article/87d1b25e89b0436aa5d1c86c84ab1763

The manifestations of rare organ sarcoidosis

Autor: Marc A. Judson, Jean Pastre, Dominique Israël-Biet

Publikováno v: Sarcoidosis ISBN: 9781849841450

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_________::bab2d301419ee965c842d7bb1ece3b20
https://doi.org/10.1183/2312508x.10033320

ERS clinical practice guidelines on treatment of sarcoidosis

Autor: Jan C. Grutters, Alexander G. Mathioudakis, Ginger Spitzer, Bernd Quadder, Marc A. Judson, Daniel A. Culver, Thomy Tonia, Elyse E. Lower, Robert P. Baughman, Peter Korsten, Francesco Bonella, Athol U. Wells, Dominique Israël-Biet, Dominique Valeyre, Katerina M. Antoniou, Hiliaro Nunes, Daniel R. Ouellette, Filippo Martone, Marjolein Drent, Wim A. Wuyts, David Rigau, Paola Rottoli, Blin Nagavci

Publikováno v: EUROPEAN RESPIRATORY JOURNAL
r-IIB SANT PAU. Repositorio Institucional de Producción Científica del Instituto de Investigación Biomédica Sant Pau
instname
European Respiratory Journal, 58(6):2004079. European Respiratory Society

Background The major reasons to treat sarcoidosis are to lower the morbidity and mortality risk or to improve quality of life (QoL). The indication for treatment varies depending on which manifestation is the cause of symptoms: lungs, heart, brain, s

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::972ec1de2a247f10f41d992f3f3b658d
https://doi.org/10.1183/13993003.04079-2020

Interstitial lung diseases associated with mutations of poly(A)-specific ribonuclease: A multicentre retrospective study

Autor: Quentin, Philippot, Caroline, Kannengiesser, Marie Pierre, Debray, Clément, Gauvain, Ibrahima, Ba, Margherita, Vieri, Anne, Gondouin, Jean-Marc, Naccache, Martine, Reynaud-Gaubert, Yurdagul, Uzunhan, Benjamin, Bondue, Dominique, Israël-Biet, Philippe, Dieudé, Cécile, Fourrage, Elodie, Lainey, Effrosyne, Manali, Spyros, Papiris, Lidwine, Wemeau, Sandrine, Hirschi, Hervé, Mal, Hilario, Nunes, Frédéric, Schlemmer, Elodie, Blanchard, Fabian, Beier, Vincent, Cottin, Bruno, Crestani, Raphaël, Borie

Publikováno v: Respirology (Carlton, Vic.)REFERENCES. 27(3)

Poly(A)-specific ribonuclease (PARN) mutations have been associated with familial pulmonary fibrosis. This study aims to describe the phenotype of patients with interstitial lung disease (ILD) and heterozygous PARN mutations.We performed a retrospect

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::a8501f62b582b497ace869cf4558cf2d
https://pubmed.ncbi.nlm.nih.gov/34981600