Prevalence, management and efficacy of treatment in portal vein obstruction after paediatric liver transplantation: protocol of the retrospective international multicentre PORTAL registry

Autor: Barbara E Wildhaber, Martin de Santibañes, Victoria Ardiles, Ruben H J de Kleine, Raj Prasad, Bhargava Mullapudi, Jai Patel, Reinoud P H Bokkers, Ekkehard Sturm, Simon McGuirk, Girish Gupte, John McCall, Richard J Hendrickson, Winita Hardikar, Helen Evans, Khalid Sharif, Marumbo Mtegha, Amar Mukund, David Duncan, Emmanuel Gonzales, Marco Spada, Mureo Kasahara, Denise Aldrian, Bader A Alfares, Hubert P J van der Doef, Thomas Casswall, Greg Nowak, Martin Delle, Valeria Berchtold, Georg F Vogel, Piotr Kaliciński, Malgorzata Markiewicz-Kijewska, Adam Kolesnik, Jesús Q Bernabeu, María Mercadal Hally, Mauricio Larrarte K, Paolo Marra, Michela Bravi, Domenico Pinelli, Seisuke Sakamoto, Hajime Uchida, Vidyadhar Mali, Marion Aw, Stéphanie Franchi-Abella, Florent Guérin, Guillermo Cervio, Julia Minetto, Sergio Sierre, Jimmy Walker Uno, Steffen Hartleif, Cristina T Ferreira, Luiza S Nader, Marco Farina, Catalina Jaramillo, Manuel I Rodriguez-Davalos, Peter Feola, Amit A Shah, Phoebe M Wood, Michael R Acord, Ryan T Fischer, Rajeev Khanna, Viniyendra Pamecha, Gilda Porta, Tommaso Alterio, Giuseppe Maggiore, Marisa Beretta, Rudi Dierckx

Publikováno v: BMJ Open, Vol 13, Iss 7 (2023)

Introduction Portal vein obstruction (PVO) consists of anastomotic stenosis and thrombosis, which occurs due to a progression of the former. The aim of this large-scale international study is to assess the prevalence, current management practices and

Externí odkaz: https://doaj.org/article/0bed8fe8879b4abe89157619e252beb9

Internal Ileal Diversion as Treatment for Progressive Familial Intrahepatic Cholestasis Type 1-Associated Graft Inflammation and Steatosis after Liver Transplantation

Autor: Anna M. Kavallar, Franka Messner, Stefan Scheidl, Rupert Oberhuber, Stefan Schneeberger, Denise Aldrian, Valeria Berchtold, Murat Sanal, Andreas Entenmann, Simon Straub, Anna Gasser, Andreas R. Janecke, Thomas Müller, Georg F. Vogel

Publikováno v: Children, Vol 9, Iss 12, p 1964 (2022)

Background: Progressive Familial Intrahepatic cholestasis type I (PFIC1) is a rare congenital hepatopathy causing cholestasis with progressive liver disease. Surgical interruption of the enterohepatic circulation, e.g., surgical biliary diversion (SB

Externí odkaz: https://doaj.org/article/3f6935a47f1e4c8bb488a1303a8fa774

Influence of early biliary complications on survival rates after pediatric liver transplantation-A positive outlook

Autor: Andreas Entenmann, Stefan Schneeberger, Dietmar Öfner, Hanno Ulmer, Christian Margreiter, Franka Messner, Georg F. Vogel, Johanna Krapf, Thomas Müller, Denise Aldrian, Raimund Margreiter, Rupert Oberhuber, Valeria Berchtold, Benno Cardini, Annemarie Weissenbacher, Hans J. Schlitt

Publikováno v: Pediatric transplantationREFERENCES. 25(7)

BACKGROUND Early biliary complications (EBC) constitute a burden after pediatric liver transplantation frequently requiring immediate therapy. We aimed to assess the impact of EBC on short- and long-term patient and graft survival as well as post-tra

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::aa0c6e564df3e4df269b9c4515a5e0a1
https://pubmed.ncbi.nlm.nih.gov/34185384

Congenital Diarrhea and Cholestatic Liver Disease: Phenotypic Spectrum Associated with MYO5B Mutations

Autor: S Ünal, J Koeglmeier, M Meissl, H Ayyıldız Civan, J Melek, T Siahanidou, A M Demir, Patrick Gerner, J H Montoya, Duba H-C., Denise Aldrian, A Koutroumpa, Sahar Mansour, Michael W. Hess, Murat Cakir, Georg F. Vogel, Thomas Müller, J Hornova, T K Frey, Aysel Ünlüsoy Aksu, Y Rachman, Ekkehard Sturm, Andreas R. Janecke, G Düker, M Miqdady, Lukas A. Huber, R Lima, Frank M. Ruemmele, Carsten Posovszky, J Hertecant, Holm H. Uhlig, E Ramos Boluda, Stefan Wirth, Raffi Lev-Tzion, C Deppisch, R Lanzersdorfer, Merit M. Tabbers, Simone Kathemann, Yaron Avitzur

Publikováno v: Journal of Clinical Medicine, Vol 10, Iss 481, p 481 (2021)
Journal of clinical medicine, 10(3):481, 1-15. Multidisciplinary Digital Publishing Institute (MDPI)
Journal of Clinical Medicine
Volume 10
Issue 3

Myosin Vb (MYO5B) is a motor protein that facilitates protein trafficking and recycling in polarized cells by RAB11- and RAB8-dependent mechanisms. Biallelic MYO5B mutations are identified in the majority of patients with microvillus inclusion diseas

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::8a378cf582516dca7504ff713f219f8f
https://www.mdpi.com/2077-0383/10/3/481