Secondary coenzyme Q10 deficiency and oxidative stress in cultured fibroblasts from patients with riboflavin responsive multiple Acyl-CoA dehydrogenation deficiency

Autor: Frank E. Frerman, Paula Fernandez Guerra, John Land, Colleen M. Byron, Nanna Cornelius, Weston W Radford, Thomas J. Corydon, Ian P. Hargreaves, Niels Gregersen, Rikke Katrine Jentoft Olsen, Andrea K Furdek

Publikováno v: Cornelius, N, Byron, C, Hargreaves, I, Guerra, P F, Furdek, A K, Land, J, Radford, W W, Frerman, F, Corydon, T J, Gregersen, N & Olsen, R K J 2013, ' Secondary coenzyme Q10 deficiency and oxidative stress in cultured fibroblasts from patients with riboflavin responsive multiple Acyl-CoA dehydrogenation deficiency ', Human Molecular Genetics, vol. 22, no. 19, pp. 3819-27 . https://doi.org/10.1093/hmg/ddt232

Coenzyme Q10 (CoQ10) is essential for the energy production of the cells and as an electron transporter in the mitochondrial respiratory chain. CoQ10 links the mitochondrial fatty acid β-oxidation to the respiratory chain by accepting electrons from

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::141c2347e770f58c8f77ad031f73fa2a
https://pure.au.dk/portal/da/publications/secondary-coenzyme-q10-deficiency-and-oxidative-stress-in-cultured-fibroblasts-from-patients-with-riboflavin-responsive-multiple-acylcoa-dehydrogenation-deficiency(e7212f6e-3c6b-4366-b7a9-9984f45ab2b2).html

An error in reporting errors

Autor: Colleen M. Byron

Publikováno v: Journal of Chemical Education. 70:432

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_________::532fbf2b42ad93c41bd75df11b87dd07
https://doi.org/10.1021/ed070p432.3

Unusual redox properties of electron-transfer flavoprotein from Methylophilus methylotrophus

Autor: Victor L. Davidson, Mazhar Husain, Marian T. Stankovich, Colleen M. Byron

Publikováno v: Biochemistry. 28(21)

The most positive redox potential ever recorded for a flavin adenine dinucleotide (FAD) containing protein has been measured for an electron-transfer flavoprotein (ETF) synthesized by Methylophilus methylotrophus. This potential value, 0.196 V versus

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::e15a092eecc78d004896831713b1b9be
https://pubmed.ncbi.nlm.nih.gov/2605209