Fatal Exacerbations of Systemic Capillary Leak Syndrome Complicating Coronavirus Disease

Autor: Patricia C. Cheung, A. Robin Eisch, Noble Maleque, Derek M. Polly, Sara C. Auld, Kirk M. Druey

Publikováno v: Emerging Infectious Diseases, Vol 27, Iss 10, Pp 2529-2534 (2021)

We report 2 fatal exacerbations of systemic capillary leak syndrome (SCLS), also known as Clarkson disease, associated with coronavirus disease (COVID-19) in the United States. One patient carried an established diagnosis of SCLS and the other sought

Externí odkaz: https://doaj.org/article/54762730bae046fbb9812118069e0165

Chronic idiopathic systemic capillary leak syndrome: a case report

Autor: Ahmed M. Alkhunaizi, Abdullah H. Kabbani, Mohamed A. ElTigani

Publikováno v: Allergy, Asthma & Clinical Immunology, Vol 15, Iss 1, Pp 1-4 (2019)

Abstract Background Idiopathic systemic capillary leak syndrome (ISCLS), is a rare disorder characterized by recurrent attacks of varying severity of hypovolemic shock and generalized edema in association with hemoconcentration and hypoalbuminemia in

Externí odkaz: https://doaj.org/article/df56f0825ca64ea28da72435ac7c0877

Fatal Systemic Capillary Leak Syndrome after SARS-CoV-2Vaccination in Patient with Multiple Myeloma

Autor: Yeon Haw Jung, Gwang Jun Choi, Jung Ho Kim, Dong Keun Kim, Sejoong Kim, Junmo Kim, Geun Yong Kwon, Seon Ha Baek

Publikováno v: Emerging Infectious Diseases
Emerging Infectious Diseases, Vol 27, Iss 11, Pp 2973-2975 (2021)

A young man with smoldering multiple myeloma died of hypotensive shock 2.5 days after severe acute respiratory syndrome coronavirus 2 vaccination. Clinical findings suggested systemic capillary leak syndrome (SCLS); the patient had experienced a prev

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::05d6902ffa1d5683bbb6e50a47d4d6af
https://pubmed.ncbi.nlm.nih.gov/34459725

Intravenous Immunoglobulins Tapering and Withdrawal in Systemic Capillary Leak Syndrome (Clarkson Disease)

Autor: Quentin Moyon, Marc Pineton de Chambrun, Marie Gousseff, Alexis Mathian, Miguel Hie, Geoffrey Urbanski, Franco Verlicchi, Stanislas Faguer, Antoine Dossier, Jean-Christophe Lega, Sophie Riviere, David Saadoun, Julie Graveleau, Marie-Josée Lucchini-Lecomte, Christine Christides, Sylvie Le Moal, Béatrice Bibes, Giuseppe Malizia, Marc Ruivard, Gilles Blaison, Laurent Alric, Christian Agard, Martin Soubrier, Jean-François Viallard, Hervé Levesque, Georges-Etienne Rivard, Nathalie Tieulie, Arnaud Hot, Pierre-Yves Lovey, Thomas Hanslik, François Lhote, Vincent Eble, Jorge Álvarez Troncoso, Avinash Aujayeb, Paul Quentric, Dov Taieb, Fleur Cohen-Aubart, Marc Lambert, Zahir Amoura

Publikováno v: Journal of Allergy and Clinical Immunology: In Practice
Journal of Allergy and Clinical Immunology: In Practice, 2022, 10 (11), pp.2889-2895. ⟨10.1016/j.jaip.2022.07.006⟩

International audience; Background: The systemic capillary leak syndrome (SCLS), also known as Clarkson disease, is a very rare condition characterized by recurrent life-threatening episodes of vascular hyperpermeability in the presence of a monoclon

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::ff37f7eee45f0767c8bd973b3e66e933
https://hal.science/hal-03888981

Neutrophil activation in systemic capillary leak syndrome (Clarkson disease)

Autor: Zhihui Xie, Xuesong Gu, John I. Gallin, Hasan H. Otu, Towia A. Libermann, Kirk M. Druey, Douglas B. Kuhns, Samir M. Parikh

Publikováno v: Journal of Cellular and Molecular Medicine

Systemic capillary leak syndrome (SCLS; Clarkson disease) is a rare orphan disorder characterized by transient yet recurrent episodes of hypotension and peripheral oedema due to diffuse vascular leakage of fluids and proteins into soft tissues. Humor

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::1031f655cc7ac4c7fcbfe206227bdac7
http://europepmc.org/articles/PMC6653644