Zobrazeno 1 - 7
of 7
pro vyhledávání: '"Christophe Bourgoin"'
Autor:
Audrey Arfi, Christophe Bourgoin, Luisa Basso, Carla Emiliani, Brunella Tancini, Vanna Chigorno, Yu-Teh Li, Aldo Orlacchio, Livia Poenaru, Sandro Sonnino, Catherine Caillaud
Publikováno v:
Neurobiology of Disease, Vol 20, Iss 2, Pp 583-593 (2005)
Sandhoff disease is an autosomal recessive neurodegenerative disease characterized by a GM2 ganglioside intralysosomal accumulation. It is due to mutations in the β-hexosaminidases β-chain gene, resulting in a β-hexosaminidases A (αβ) and B (β
Externí odkaz:
https://doaj.org/article/1c15f697f70d4d478e2e1452183d9fa9
Autor:
Jean-Christophe Bourgoin
Publikováno v:
Annals of Global Analysis and Geometry. 32:1-13
In this paper, we study the minimality of the map \(\frac{x}{\|x\|}\) for the weighted energy functional \(E_{f,p}= \int_{\mathbf{B}^n}f(r)\|\nabla u\|^p dx\), where \(f : [0,1] \rightarrow \mathbb{R}^{+}\) is a continuous function. We prove that for
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::23c517a040e8e58cef6b1228a66cd000
https://doi.org/10.1007/s10455-006-9049-1
https://doi.org/10.1007/s10455-006-9049-1
Autor:
Christophe Bourgoin, Livia Poenaru, Brunella Tancini, Audrey Arfi, Vanna Chigorno, Carla Emiliani, Catherine Caillaud, Sandro Sonnino, Yu-Teh Li, Luisa Basso, Aldo Orlacchio
Publikováno v:
Neurobiology of Disease, Vol 20, Iss 2, Pp 583-593 (2005)
Sandhoff disease is an autosomal recessive neurodegenerative disease characterized by a GM2 ganglioside intralysosomal accumulation. It is due to mutations in the beta-hexosaminidases beta-chain gene, resulting in a beta-hexosaminidases A (alphabeta)
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::1d6939b1abeb0ab4150b2a57c48c5d20
http://www.sciencedirect.com/science/article/pii/S0969996105001336
http://www.sciencedirect.com/science/article/pii/S0969996105001336
Autor:
Livia Poenaru, Brunella Tancini, A Gelot, Christophe Bourgoin, Ra Gravel, Ej Kremer, Catherine Caillaud, Cristina Drugan, Aldo Orlacchio, Carla Emiliani
Publikováno v:
Gene Therapy
Gene Therapy, Nature Publishing Group, 2003, 10 (21), pp.1841--1849. ⟨10.1038/sj.gt.3302081⟩
Gene Therapy, 2003, 10 (21), pp.1841--1849. ⟨10.1038/sj.gt.3302081⟩
Gene Therapy, Nature Publishing Group, 2003, 10 (21), pp.1841--1849. ⟨10.1038/sj.gt.3302081⟩
Gene Therapy, 2003, 10 (21), pp.1841--1849. ⟨10.1038/sj.gt.3302081⟩
Sandhoff disease is a severe inherited neurodegenerative disorder resulting from deficiency of the beta-subunit of hexosaminidases A and B, lysosomal hydrolases involved in the degradation of G(M2) ganglioside and related metabolites. Currently, ther
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::ddbb8c9261261b0c8cf29bc162145601
https://hal.archives-ouvertes.fr/hal-02239680
https://hal.archives-ouvertes.fr/hal-02239680
Autor:
Audrey Arfi, Christophe Bourgoin, Luisa Basso, Sandro Sonnino, Catherine Caillaud, Livia Poenaru
Publikováno v:
Molecular Therapy. 9:S331
Sandhoff disease is an autosomal recessive neurodegenerative disease characterized by the intralysosomal accumulation of GM2 ganglioside. It is due to mutations in the hexosaminidases β-chain gene, resulting in a hexosaminidases A (αβ) and B (ββ
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::bce252d76a6dd697c64d6f59f743be57
https://doi.org/10.1016/j.ymthe.2004.06.777
https://doi.org/10.1016/j.ymthe.2004.06.777
for weighted energy.
Autor:
Jean-Christophe Bourgoin
Publikováno v:
Annals of Global Analysis & Geometry; Aug2007, Vol. 32 Issue 1, p1-13, 13p
Autor:
Jean-Christophe Bourgoin
Publikováno v:
Journal of Mathematical Analysis and Applications. (2):1199-1208
In this paper, we investigate minimizing properties of the map $x/\|x\|$ from the Euclidean unit ball $\mathbf{B}^{n}$ to its boundary $\mathbb{S}^{n-1}$, for the weighted energy functionals $E^n\_{p,\alpha}(u)=\int\_{\mathbf{B}^{n}} \|x\|^{\alpha}\|
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::0267a27dd985be4544b011eb589a25b9