Zobrazeno 1 - 8
of 8
pro vyhledávání: '"B G, Bolscher"'
Autor:
M, de Boer, B G, Bolscher, M C, Dinauer, S H, Orkin, C I, Smith, A, Ahlin, R S, Weening, D, Roos
Publikováno v:
Blood. 80:1553-1558
Chronic granulomatous disease (CGD) is characterized by the absence of a respiratory burst in activated phagocytes. Defects in at least four different genes lead to CGD. Patients with the X-linked form of CGD have mutations in the gene for the beta-s
Publikováno v:
Nederlands tijdschrift voor geneeskunde. 139(44)
Assay of spectrin in erythrocytes as a diagnostic test in hereditary spherocytosis (HS).Validation of a diagnostic test.Central Laboratory of the Netherlands Red Cross Blood Transfusion Service in Amsterdam, the Netherlands.A radiolabelled rabbit ant
Publikováno v:
Immunodeficiency. 4(1-4)
Publikováno v:
The Journal of biological chemistry. 266(36)
The effects of the chaotropic agent, guanidine HCl, on the chlorinating activity, optical absorption, EPR, and resonance Raman spectra of myeloperoxidase have been studied. In the presence of the agent the Soret optical absorption of the reduced enzy
Publikováno v:
Blood. 77(11)
The NADPH:O2 oxidoreductase of phagocytic leukocytes is an important enzyme for the bactericidal activity of these cells. Cytochrome b558 is a membrane component of this enzyme. In X-linked chronic granulomatous disease (Xb- CGD) the phagocytes are d
Publikováno v:
The Journal of biological chemistry. 265(26)
Neutrophil NADPH:O2 oxidoreductase activity, essential in the killing of bacteria by neutrophils, can be elicited in a cell-free system that requires plasma membranes, cytosol and sodium dodecyl sulfate. In addition, GTP or its nonhydrolyzable analog
Publikováno v:
Acta paediatrica Hungarica. 29(1-2)
Autor:
A J, Verhoeven, B G, Bolscher, L J, Meerhof, R, van Zwieten, J, Keijer, R S, Weening, D, Roos
Publikováno v:
Blood. 73(6)
Monoclonal antibodies (MoAbs) were raised against cytochrome b558, a membrane-bound component of the NADPH:O2 oxidoreductase in human neutrophils. This cytochrome consists of a low-molecular-weight (low-mol-wt) subunit of 22 to 23 Kd, probably encode