Zobrazeno 1 - 10
of 472
pro vyhledávání: '"Andrew R, Gennery"'
Autor:
Martin Carby, Jasvir Parmar, Andrew Bryant, Thomas Chadwick, Luke Vale, Catherine Exley, Andrew J Fisher, Helen Hancock, Richard Thompson, Joanne Lally, Andrew R Gennery, Michelle Bardgett, Siân Russell, Michael White, James MS Wason, Nicola Goudie, Anneka Kershaw, Julia Phillipson, Alex Bevin-Nicholls, Hesther Smith, Laura Frisby, Rebecca Errington, Karthik Santhanakrishnan
Publikováno v:
BMJ Open Respiratory Research, Vol 11, Iss 1 (2024)
Background Long-term survival after lung transplantation is limited compared with other organ transplants. The main cause is development of progressive immune-mediated damage to the lung allograft. This damage, which can develop via multiple immune p
Externí odkaz:
https://doaj.org/article/25ff32a40f734970b727cb09b3679576
Publikováno v:
Frontiers in Immunology, Vol 14 (2023)
Primary immune regulatory disorders (PIRDs) are inborn errors of immunity caused by a loss in the regulatory mechanism of the inflammatory or immune response, leading to impaired immunological tolerance or an exuberant inflammatory response to variou
Externí odkaz:
https://doaj.org/article/4030ae7db81d42ec8d6b94bad2d99a8a
Autor:
Gareth Parry, Zdenka Reinhardt, Abbas Khushnood, Andrew R Gennery, Chris M Bacon, Jacob Simmonds, Ugonna T Offor, Paolo Hollis, Milos Ognjanovic, Heather M Long, Simon Bomken
Publikováno v:
BMJ Open, Vol 13, Iss 10 (2023)
Introduction Paediatric heart transplant patients are disproportionately affected by Epstein-Barr virus (EBV)-related post-transplant lymphoproliferative disease (PTLD) compared with other childhood solid organ recipients. The drivers for this dispar
Externí odkaz:
https://doaj.org/article/05b4b630bb3941479894778fe024d9a9
Publikováno v:
Journal of Clinical Medicine, Vol 13, Iss 4, p 1092 (2024)
Chronic granulomatous disease (CGD) is a rare inborn error of immunity that typically manifests with infectious complications. As the name suggest though, inflammatory complications are also common, often affecting the gastrointestinal, respiratory,
Externí odkaz:
https://doaj.org/article/9512585a5563401e9c8f74eef867a89b
Autor:
Jerold Jeyaratnam, Maura Faraci, Andrew R. Gennery, Katarzyna Drabko, Mattia Algeri, Akira Morimoto, Tiarlan Sirait, Arjan C. Lankester, Michael Albert, Benedicte Neven, Joost Frenkel, on behalf of the EBMT Inborn Errors Working Party
Publikováno v:
Pediatric Rheumatology Online Journal, Vol 20, Iss 1, Pp 1-8 (2022)
Abstract Objectives Mevalonate kinase deficiency (MKD) is a rare autoinflammatory syndrome. Several reports have described allogeneic hematopoietic stem cell transplantation in severely affected patients, sometimes with promising results. In view of
Externí odkaz:
https://doaj.org/article/390bed8901194b8ebf45ecb4e8ff728a
Publikováno v:
Frontiers in Pediatrics, Vol 11 (2023)
Externí odkaz:
https://doaj.org/article/62ab0b285871410ab5d44df79257d6e3
Autor:
Ines Bojanic, Nina Worel, Carolina P. Pacini, Georg Stary, Agnieszka Piekarska, Aisling M. Flinn, Kimberly J. Schell, Andrew R. Gennery, Robert Knobler, João F. Lacerda, Hildegard T. Greinix, Drazen Pulanic, Rachel E. Crossland
Publikováno v:
Frontiers in Immunology, Vol 14 (2023)
Haematopoietic stem cell transplantation (HSCT) is the treatment of choice for malignant haematological diseases. Despite continuous improvements in pre- and post-transplantation procedures, the applicability of allo-HSCT is limited by life-threateni
Externí odkaz:
https://doaj.org/article/c94a325df4744cc9a0f8e259d3242b5d
Autor:
Aisling M. Flinn, Andrew R. Gennery
Publikováno v:
Orphanet Journal of Rare Diseases, Vol 17, Iss 1, Pp 1-9 (2022)
Abstract Primary Immune Regulatory Disorders (PIRD) describe a group of conditions characterized by loss of normal inflammatory control and immune tolerance mechanisms, with autoimmunity as a predominant clinical feature. PIRD can arise due to defect
Externí odkaz:
https://doaj.org/article/a4d1e70482174d01b7f530dbb8910ab7
Publikováno v:
Frontiers in Immunology, Vol 13 (2022)
Externí odkaz:
https://doaj.org/article/397e2f8d444b4b78a5441580be1ecfa6
Publikováno v:
Frontiers in Pediatrics, Vol 10 (2022)
ObjectiveThis study aims to assess the performance of biomarkers used for the prediction of bacterial, viral, and fungal infection in immunocompromised children upon presentation with fever.MethodsWe performed a literature search using PubMed and MED
Externí odkaz:
https://doaj.org/article/93e44003f7904d5ba0aa331275fcb2fb