Zobrazeno 1 - 7
of 7
pro vyhledávání: '"Alexey Pshonkin"'
Autor:
Guenter Henze, Ekaterina Mikhailova, Alexander Popov, Julia Roumiantseva, Oleg Budanov, Svetlana Lagoyko, Liudmila Zharikova, Natalia Miakova, Dmitry Litvinov, Lili Khachatryan, Alexey Pshonkin, Natalia Ponomareva, Elmira Boichenko, Svetlana Varfolomeeva, Julia Dinikina, Galina Novichkova, Alexander Karachunskiy
Publikováno v:
Journal for ImmunoTherapy of Cancer, Vol 12, Iss 6 (2024)
The bispecific T cell-binding antibody blinatumomab (CD19/CD3) is widely and successfully used for the treatment of children with relapsed or refractory B-cell precursor acute lymphoblastic leukemia (BCP-ALL). Here, we report the efficacy of a single
Externí odkaz:
https://doaj.org/article/df13223cf72b4f50af1be617fa311e73
Autor:
Galina Ovsyannikova, Anna Pavlova, Ekaterina Deordieva, Elena Raykina, Alexey Pshonkin, Alexey Maschan, Michael Maschan
Publikováno v:
Frontiers in Pediatrics, Vol 10 (2022)
GATA2 deficiency is one of the most common predisposing conditions for MDS in young individuals. It is characterized by autosomal dominant inheritance and a high rate of de novo mutations. Here we describe the clinical phenotype and hematological pre
Externí odkaz:
https://doaj.org/article/ac8c50cc7935454b9740dbde94e98a32
Autor:
Olga Goronkova, Galina Novichkova, Tatiana Salimova, Irina Kalinina, Dina Baidildina, Ulyana Petrova, Kristina Antonova, Maria Sadovskaya, Elena Suntsova, Dmitry Evseev, Victor Matveev, Dmitry Venyov, Lili Khachatryan, Dmitry Litvinov, Alexey Pshonkin, Galina Ovsyannikova, Natalia Kotskaya, Darina Gobadze, Yulia Olshanskaya, Alexander Popov, Elena Raykina, Olga Mironenko, Kirill Voronin, Bazarma Purbueva, Elmira Boichenko, Yulia Dinikina, Evgeniya Guseynova, Dmitry Sherstnev, Elena Kalinina, Sergey Mezentsev, Olga Streneva, Natalia Yudina, Olga Plaksina, Elena Erega, Michael Maschan, Alexey Maschan
Publikováno v:
Blood Advances. 7:953-962
We compared the efficacy and safety of eltrombopag (ELTR) combined with immunosuppressive therapy (IST) and IST alone in treatment-naïve children with severe (SAA) and very severe (vSAA) aplastic anemia. Ninety-eight pediatric patients were randomiz
Autor:
Alexander Poletaev, Alexey Pshonkin, Pavel Zharkov, Dmitry Florinskiy, Daria Fedorova, Elena Seregina, Pavel Levin
Publikováno v:
Pediatria. Journal named after G.N. Speransky. 101:50-55
Factor XII deficiency is a non-hemorrhagic coagulopathy resulting in prolonged in vitro clotting time. At the same time, in our country there are cases when patients with factor XII deficiency receive preventive fresh frozen plasma before surgical tr
Autor:
Alexander Poletaev, Alexey Pshonkin, Pavel Zharkov, Dmitry Florinskiy, Daria Fedorova, Elena Seregina
Publikováno v:
Pediatric Hematology/Oncology and Immunopathology. 21:104-109
Congenital combined vitamin K-dependent clotting factors deficiency is an extremely rare bleeding disorder, a few cases have been described worldwide. This coagulopathy requires a differential diagnosis with vitamin K deficiency bleeding of the newbo
Autor:
Daria Fedorova, Galina Ovsyannikova, Maria Kurnikova, Anna Pavlova, Tatiana Konyukhova, Alexey Pshonkin, Nataliya Smetanina
Publikováno v:
Pediatric Blood & Cancer. 69
Diamond-Blackfan anemia (DBA) is an inherited bone marrow failure syndrome, associated with mutations in ribosomal protein (RP) genes. Growing data on mutations in non-RP genes in patients with DBA-like phenotype became available over recent years. W
Autor:
Galina Ovsyannikova, Anna Pavlova, Ekaterina Deordieva, Elena Raykina, Alexey Pshonkin, Alexey Maschan, Michael Maschan
Publikováno v:
Frontiers in pediatrics. 10
GATA2 deficiency is one of the most common predisposing conditions for MDS in young individuals. It is characterized by autosomal dominant inheritance and a high rate of de novo mutations. Here we describe the clinical phenotype and hematological pre