Zobrazeno 1 - 10
of 11
pro vyhledávání: '"Akifumi Sakata"'
Late-onset cases of familial hemophagocytic lymphohistiocytosis with missenseperforin gene mutations
Autor:
Akifumi Sakata, Yumi Kurokawa, Shinsaku Imashuku, Kenichi Koike, Akira Morimoto, Takashi Fukushima, Tsutomu Matsumora, Eiichi Ishii, Ikuyo Ueda, Shuichi Ito
Publikováno v:
American Journal of Hematology. 82:427-432
Since the discovery of perforin gene mutations in familial hemophagocytic lymphohistiocytosis (FHL) type 2, heterogeneous features in FHL2 patients have been identified in a report of Feldmann et al. as the beginning. This study was conducted to dete
Autor:
Akihisa, Sawada, Naoki, Sakata, Banryoku, Higuchi, Yasufumi, Takeshita, Takashi, Ishihara, Akifumi, Sakata, Masahiko, Kouroki, Osamu, Kondo, Maho, Koyama, Shinya, Hirano, Masahiro, Yasui, Masami, Inoue, Akira, Yoshioka, Keisei, Kawa
Publikováno v:
[Rinsho ketsueki] The Japanese journal of clinical hematology. 50(12)
Invasive fungal infection (IFI) is a serious complication of chemotherapy for hematological malignancies and autologous/allogeneic hematopoietic stem cell transplantation in children and shows a high mortality rate. We performed a randomized trial co
Autor:
Masami, Inoue, Masahiro, Yasui, Akihisa, Sawada, Maho, Koyama, Akifumi, Sakata, Yasufumi, Takeshita, Masahiko, Kouroki, Takayuki, Okamura, Naoki, Sakata, Keisei, Kawa
Publikováno v:
[Rinsho ketsueki] The Japanese journal of clinical hematology. 47(11)
We report the results of 39 children who underwent cord blood stem cell transplantation (CBSCT) at our institute during the period from February 1996 to July 2005. The patients consisted of 9 with non-malignant disease, 26 with malignant disease and
Autor:
Yasufumi Takeshita, Ji Yoo Kim, Emiko Sato, Shigenori Kusuki, Maho Koyama, Naoki Sakata, Akifumi Sakata, Keisei Kawa, Takayuki Okamura, Masami Inoue, Banryoku Higuchi, Akihisa Sawada, Masahiro Yasui
Publikováno v:
American journal of hematology. 81(8)
Epstein-Barr virus (EBV) occasionally infects T and NK cells and causes EBV-infected T/NK-cell lymphoproliferative disease (LPD), which comprises chronic active EBV infection, EBV-associated hemophagocytic syndrome, mosquito allergy, hydroa vaccinifo
Autor:
Masahiro Yasui, Akihisa Sawada, Yasufumi Takeshita, Keisei Kawa, Masami Inoue, Akifumi Sakata, Maho Koyama, Takayuki Okamura
Publikováno v:
International journal of hematology. 82(5)
Recent findings indicate that Epstein-Barr virus (EBV)-infected T-/natural killer (NK) cells play an important role in the pathogenesis of mosquito allergy, and most patients with mosquito allergy die early in life if not properly treated. Over the l
Publikováno v:
[Rinsho ketsueki] The Japanese journal of clinical hematology. 46(6)
Autor:
Yasufumi Takeshita, Masami Inoue, Masahiro Yasui, Takayuki Okamura, Akihisa Sawada, K Yagi, Masahiko Kouroki, Naoki Sakata, Keisei Kawa, Maho Koyama, Akifumi Sakata
Publikováno v:
Bone marrow transplantation. 37(6)
Eight children underwent reduced-intensity stem cell transplantation (RIST) from an HLA-matched sibling. They received a fludarabine-melphalan based preparative regimen. Stem cell source was bone marrow, and GVHD prophylaxis consisted of cyclosporine
Autor:
Hidetoshi Takada, Masahiro Sako, Akifumi Sakata, Toshiro Hara, Kenichi Koike, Shouichi Ohga, Takehiko Sasazuki, Hisanori Horiuchi, Kenji Furuno, Shinsaku Imashuku, Akira Morimoto, Masaki Yasukawa, Ken Yamamoto, Yoshiyasu Ogata, Eiichi Ishii, Ikuyo Ueda, Miyoko Imayoshi, Ryutaro Shirakawa, Masafumi Zaitsu
Publikováno v:
Blood. 105(9)
Mutations of the perforin (PRF1) and MUNC13-4 genes distinguish 2 forms of familial hemophagocytic lymphohistiocytosis (FHL2 and FHL3, respectively), but the clinical and biologic correlates of these genotypes remain in question. We studied the prese
Autor:
Takayuki Okamura, Yasufumi Takeshita, Masami Inoue, Keisei Kawa, Akihisa Sawada, Masahiro Yasui, T Nakano, Maho Koyama, Akifumi Sakata
Publikováno v:
Bone Marrow Transplantation. 36:453-454
Successful treatment of JMML with related bone marrow transplantation after reduced-intensity conditioning
Autor:
Akihisa Sawada, Emiko Sato, Maho Koyama, Banryoku Higuchi, Shigenori Kusuki, Ji Yoo Kim, Yasufumi Takeshita, Akifumi Sakata, Naoki Sakata, Takayuki Okamura, Masahiro Yasui, Masami Inoue, Keisei Kawa
Publikováno v:
American Journal of Hematology; Aug2006, Vol. 81 Issue 8, p576-581, 6p