Zobrazeno 1 - 10
of 3 049
pro vyhledávání: '"Adult-onset Still's disease"'
Publikováno v:
Immunological Medicine, Pp 1-5 (2024)
Elevated liver enzymes are commonly observed among adult-onset Still’s disease (AOSD), but severe acute liver failure is extremely rare. Although severe acute liver failure associated with AOSD poses a life-threatening condition, the appropriate tr
Externí odkaz:
https://doaj.org/article/1e4f7681f0c5433db2b8328296cd726c
Autor:
Patrick Brossard, Christian Laveille
Publikováno v:
Rheumatology and Therapy, Vol 11, Iss 3, Pp 869-880 (2024)
Abstract Introduction Emapalumab is a fully human monoclonal antibody that targets free and receptor-bound interferon-gamma (IFNγ), neutralizing its biological activity. IFNγ levels differ by orders of magnitude between patients with primary hemoph
Externí odkaz:
https://doaj.org/article/3269a63113544c5fb3eb1d9820a75c89
Publikováno v:
Clinical Case Reports, Vol 12, Iss 7, Pp n/a-n/a (2024)
Key Clinical Message This case details adult‐onset Still's disease (AOSD) onset post‐human papillomavirus (HPV) vaccination and acute gastroenteritis. The timing of HPV vaccine and vaccine‐autoimmune disease literature may potentially confound
Externí odkaz:
https://doaj.org/article/e68080ea6a5a49afa780dc739e28ce50
Autor:
Valentina Myachikova, Igor Kudryavtsev, Artem Rubinstein, Arthur Aquino, Dmitry Isakov, Alexey Golovkin, Alexey Maslyanskiy
Publikováno v:
Current Issues in Molecular Biology, Vol 46, Iss 2, Pp 1177-1191 (2024)
Adult-onset Still’s disease (AOSD) is a complex systemic inflammatory disorder, categorized as an ‘IL-1 driven’ inflammasomapathy. Despite this, the interaction between T and B cells remains poorly understood. We conducted a study, enrolling 7
Externí odkaz:
https://doaj.org/article/e83c9a1ddf364f8e9745ee05db004c94
Publikováno v:
Srpski Arhiv za Celokupno Lekarstvo, Vol 152, Iss 5-6, Pp 289-292 (2024)
Introduction. Adult-onset Still’s disease (AOSD), a systemic inflammatory disorder, often represents a heterogeneous entity and diagnosis requires the exclusion of mimicking disorders, including autoinflammatory diseases. We present a patient who m
Externí odkaz:
https://doaj.org/article/a79f686c66c547909e9c472d45b39854
Autor:
Xinyue Hong, Xiaoming Wang, Ningqi Dai, Yue Sun, Honglei Liu, Xiaobing Cheng, Junna Ye, Hui Shi, Qiongyi Hu, Jianfen Meng, Zhuochao Zhou, Chengde Yang, Jialin Teng, Yutong Su, Huihui Chi
Publikováno v:
Rheumatology and Therapy, Vol 11, Iss 1, Pp 201-212 (2024)
Abstract Introduction This study aimed to characterize the morbidity, hospitalization, and mortality rates among patients with adult-onset Still’s disease (AOSD) affected by coronavirus disease 2019 (COVID-19) and explore the impact of COVID-19 on
Externí odkaz:
https://doaj.org/article/8862997af6e1413699d67e8e37cfda58
Autor:
Nawras Zayat, Avish Arora, Joselle O'Brien, Japjot Bal, Rebekah Sugarman, Leeshun Rivera, Amir Shamshirsaz, Kavita Vani, Dimitrios S. Mastrogiannis
Publikováno v:
American Journal of Perinatology Reports, Vol 14, Iss 02, Pp e145-e155 (2024)
Externí odkaz:
https://doaj.org/article/51f8eca6b9f24080aaae9af243d67d02
Autor:
Shuhei Yoshida, Tomohiro Koga, Yuya Fujita, Hiroshi Yatsuhashi, Haruki Matsumoto, Yuya Sumichika, Kenji Saito, Shuzo Sato, Tomoyuki Asano, Masao Kobayakawa, Hiromasa Ohira, Masashi Mizokami, Masaya Sugiyama, Kiyoshi Migita
Publikováno v:
Frontiers in Immunology, Vol 15 (2024)
BackgroundAutoinflammation with cytokine dysregulation may be implicated in the pathophysiology of adult-onset Still’s disease (AOSD); however, the relationship between galectins and cytokines in patients with active AOSD remains unknown. We aimed
Externí odkaz:
https://doaj.org/article/58dce78eea2f492eb201991e08f5888c
Autor:
Jinchao Jia, Mengyan Wang, Yuning Ma, Jianfen Meng, Dehao Zhu, Xia Chen, Hui Shi, Yue Sun, Honglei Liu, Xiaobing Cheng, Yutong Su, Junna Ye, Huihui Chi, Tingting Liu, Zhuochao Zhou, Fan Wang, Longfang Chen, Da Yi, Yu Xiao, Chengde Yang, Jialin Teng, Qiongyi Hu
Publikováno v:
BMC Medicine, Vol 21, Iss 1, Pp 1-15 (2023)
Abstract Background Adult-onset Still’s disease (AOSD) is a systemic autoinflammatory disease characterized by innate immune system activation, with a high risk for macrophage activation syndrome (MAS). MAS development is associated with monocyte/m
Externí odkaz:
https://doaj.org/article/609d305e94644cd2a3197714d39a78d1
Autor:
Mariana Correia Marques, Subrata Paul, Carol Lake, Ly-Lan Bergeron, Rashmi Sinha, Luciana Peixoto, Marinka Twilt, Michael J. Ombrello
Publikováno v:
Pediatric Rheumatology Online Journal, Vol 21, Iss 1, Pp 1-10 (2023)
Abstract Background Patients with systemic juvenile idiopathic arthritis (sJIA) and adult-onset Still’s disease (AOSD) have been under-represented in studies about safety of the COVID-19 immunization. We aimed to inquire about the safety and tolera
Externí odkaz:
https://doaj.org/article/2a1897924c78496fbaec7d8f86fafbbd