Zobrazeno 1 - 10
of 98
pro vyhledávání: '"AGGRESSIVE SYSTEMIC MASTOCYTOSIS"'
Autor:
D. I. Shikhbabaeva, O. Yu. Vinogradova, A. L. Neverova, M. M. Pankrashkina, M. V. Chernikov, E. O. Detkina, Yu. N. Kobzev, S. G. Malakho, V. V. Ptushkin
Publikováno v:
Онкогематология, Vol 18, Iss 4, Pp 78-89 (2023)
Background. Mastocytosis is a heterogeneous group of diseases that are characterized by excessive proliferation and accumulation of clonal (neoplastic) mast cells in one or more organs. Advanced variants of systemic mastocytosis (aggressive systemic
Externí odkaz:
https://doaj.org/article/b0824ac883044800950c5541dea6c7c5
Autor:
Makiko Tsutsumi, Hiroki Miura, Hidehito Inagaki, Yasuko Shinkai, Asuka Kato, Takema Kato, Susumu Hamada-Tsutsumi, Makito Tanaka, Kazuko Kudo, Tetsushi Yoshikawa, Hiroki Kurahashi
Publikováno v:
BMC Cancer, Vol 20, Iss 1, Pp 1-7 (2020)
Abstract Background Aggressive systemic mastocytosis (ASM) is a rare malignant disease characterized by disordered mast cell accumulation in various organs. We here describe a female ASM patient with a previous history of ovarian dysgerminoma. Method
Externí odkaz:
https://doaj.org/article/49b2a52c6fc6445689e86956d2502ecd
Publikováno v:
Blood and Lymphatic Cancer: Targets and Therapy, Vol Volume 7, Pp 25-35 (2017)
Marie Olivia Chandesris,1–3 Gandhi Damaj,1,4 Olivier Lortholary,1,3,5 Olivier Hermine1–3,6 On behalf of the CEREMAST study group 1French Reference Center for Mastocytosis (CEREMAST), 2Department of Hematology, Necker Children’s Hospital, APHP,
Externí odkaz:
https://doaj.org/article/a639a5e68fd447ebb276c6b6831a5a80
Akademický článek
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Autor:
Xiao-Yang Zhang, Wei-Hua Zhang
Publikováno v:
Cancer Biology & Medicine, Vol 11, Iss 2, Pp 134-138 (2014)
Hepatic involvement in aggressive systemic mastocytosis (ASM) is relatively common, and the main clinical features of this disease include hepatomegaly, portal hypertension, ascites, and fibrosis. Cirrhosis is a rare ASM symptom. We report an ASM cas
Externí odkaz:
https://doaj.org/article/4c423a53cbcc460fa12996f420eefbb7
Akademický článek
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Akademický článek
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Autor:
Grzegorz Helbig, Martyna Włodarczyk, Iwona Hus, Wladyslaw Gawel, Anna Łabędź, Małgorzata Raźny, Marek Rodzaj, Anna Koclęga
Publikováno v:
Indian Journal of Hematology & Blood Transfusion
Systemic mastocytosis (SM) is a rare clonal disorder with multi-organ involvements and shortened life expectancy. To date, no curative treatment for SM exists. Cladribine (2-CdA) is a purine analogue showing activity against neoplastic mast cells and
Autor:
Joseph H. Butterfield, Gunnar Nilsson, Melody C. Carter, Hanneke Oude Elberink, Bogusław Nedoszytko, Deepti Radia, Mariana Castells, Roberta Zanotti, Magdalena Lange, Cem Akin, Georg Greiner, Iván Álvarez-Twose, Javier I. Muñoz-González, Hanneke C. Kluin-Nelemans, Karin Hartmann, Peter Valent, Stephen J. Galli, Frank Siebenhaar, Karl Sotlar, Patrizia Bonadonna, Tracy I. George, Gregor Hoermann, Knut Brockow, Massimo Triggiani, Celalettin Ustun, Alberto Orfao, Lawrence B. Schwartz, Mohamad Jawhar, Sigurd Broesby-Olsen, Juliana Schwaab, Marek Niedoszytko, Wolfgang R. Sperr, Olivier Hermine, Andreas Reiter, Jason Gotlib, Selim Yavuz, Michel Arock, Dean D. Metcalfe, Hans-Peter Horny, Jonathan J. Lyons
Publikováno v:
HemaSphere, 5(11):646. LIPPINCOTT WILLIAMS & WILKINS
HemaSphere, Vol 5, Iss 11, p e646 (2021)
Valent, P, Akin, C, Hartmann, K, Alvarez-Twose, I, Brockow, K, Hermine, O, Niedoszytko, M, Schwaab, J, Lyons, J J, Carter, M C, Elberink, H O, Butterfield, J H, George, T I, Greiner, G, Ustun, C, Bonadonna, P, Sotlar, K, Nilsson, G, Jawhar, M, Siebenhaar, F, Broesby-Olsen, S, Yavuz, S, Zanotti, R, Lange, M, Nedoszytko, B, Hoermann, G, Castells, M, Radia, D H, Muñoz-Gonzalez, J I, Sperr, W R, Triggiani, M, Kluin-Nelemans, H C, Galli, S J, Schwartz, L B, Reiter, A, Orfao, A, Gotlib, J, Arock, M, Horny, H-P & Metcalfe, D D 2021, ' Updated Diagnostic Criteria and Classification of Mast Cell Disorders : A Consensus Proposal ', HemaSphere, vol. 5, no. 11, e646 . https://doi.org/10.1097/HS9.0000000000000646
HemaSphere
HemaSphere, Vol 5, Iss 11, p e646 (2021)
Valent, P, Akin, C, Hartmann, K, Alvarez-Twose, I, Brockow, K, Hermine, O, Niedoszytko, M, Schwaab, J, Lyons, J J, Carter, M C, Elberink, H O, Butterfield, J H, George, T I, Greiner, G, Ustun, C, Bonadonna, P, Sotlar, K, Nilsson, G, Jawhar, M, Siebenhaar, F, Broesby-Olsen, S, Yavuz, S, Zanotti, R, Lange, M, Nedoszytko, B, Hoermann, G, Castells, M, Radia, D H, Muñoz-Gonzalez, J I, Sperr, W R, Triggiani, M, Kluin-Nelemans, H C, Galli, S J, Schwartz, L B, Reiter, A, Orfao, A, Gotlib, J, Arock, M, Horny, H-P & Metcalfe, D D 2021, ' Updated Diagnostic Criteria and Classification of Mast Cell Disorders : A Consensus Proposal ', HemaSphere, vol. 5, no. 11, e646 . https://doi.org/10.1097/HS9.0000000000000646
HemaSphere
Mastocytosis is a hematologic neoplasm characterized by expansion and focal accumulation of neoplastic mast cells (MC) in diverse organs, including the skin, bone marrow (BM), spleen, liver, and gastrointestinal tract. The World Health Organization c
Autor:
Oliwia Bachanek-Mitura, Witold Krupski, Tomasz Gromek, Aneta Szudy-Szczyrek, Justyna Szumiło, Michał Szczyrek, Grzegorz Helbig, Karolina Chromik, Marek Hus, Zuzanna Kanduła, Andrzej Mital
Publikováno v:
Journal of Clinical Medicine
Journal of Clinical Medicine, Vol 10, Iss 1109, p 1109 (2021)
Journal of Clinical Medicine; Volume 10; Issue 5; Pages: 1109
Journal of Clinical Medicine, Vol 10, Iss 1109, p 1109 (2021)
Journal of Clinical Medicine; Volume 10; Issue 5; Pages: 1109
In April 2017 midostaurin was approved by the US Food and Drug Administration for the treatment of patients with aggressive systemic mastocytosis (ASM). So far, very limited real world data on its efficacy is available. Thirteen patients aged from 48