Zobrazeno 1 - 10
of 45
pro vyhledávání: '"A. B. Rosenbluth"'
Autor:
Ahmet Z Uluer, Gordon MacGregor, Pilar Azevedo, Veronica Indihar, Claire Keating, Marcus A Mall, Edward F McKone, Bonnie W Ramsey, Steven M Rowe, Ronald C Rubenstein, Jennifer L Taylor-Cousar, Elizabeth Tullis, Lael M Yonker, Chenghao Chu, Anna P Lam, Nitin Nair, Patrick R Sosnay, Simon Tian, Fredrick Van Goor, Lakshmi Viswanathan, David Waltz, Linda T Wang, Yingmei Xi, Joanne Billings, Alexander Horsley, Edward F. Nash, Marleen Bakker, Renske van der Meer, Petrus Merkus, Christof Majoor, Karen McCoy, Krishna Pancham, James Tolle, Bryon Quick, Ahmet Uluer, Emily DiMango, Adupa Rao, Santiago Reyes, Ross Klingsberg, Celeste Barreto, Victor Ortega, Donna Willey-Courand, Carsten Schwarz, Sivagurunathan Sutharsan, Rainald Fischer, Jane Davies, Jamie Duckers, Simon Doe, Harry Heijerman, George M. Solomon, Christian Merlo, Jennifer Griffonnet, Joseph Pilewski, Jordan Dunitz, Saba Sheikh, Ronald C. Rubenstein, Daniel B. Rosenbluth, Theodore Liou, Maria Indihar, Lael Yonker, Samya Nasr, Cynthia D. Brown, Gregory S. Sawicki, Jennifer Ruddy, Bryan Garcia, Andrew Braun, Alex H. Gifford, Nighat Mehdi, Maria Tupayachi Ortiz, Raksha Jain, Francisco J. Calimano, Jimmy Johannes, Cori L. Daines, Jason Fullmer, Joel Mermis, Christopher Barrios, Ngoc Ly, Brian P. Casserly, Stephan Eisenmann, Helge Hebestreit, Alexander Kiefer, Daniel Peckham, Martin Ledson, Eva Van Braeckel, Noel Gerard McElvaney, Edward McKone, Barry Plant, Lucy Burr, Daniel J. Smith, Peter Middleton, John Wilson
Publikováno v:
The Lancet Respiratory Medicine, 11(6), 550-562. Elsevier Limited
VX18-121-101 & VX18-561-101 Study Groups 2023, ' Safety and efficacy of vanzacaftor–tezacaftor–deutivacaftor in adults with cystic fibrosis : randomised, double-blind, controlled, phase 2 trials ', The Lancet Respiratory Medicine, vol. 11, no. 6, pp. 550-562 . https://doi.org/10.1016/S2213-2600(22)00504-5
LANCET RESPIRATORY MEDICINE
VX18-121-101 & VX18-561-101 Study Groups 2023, ' Safety and efficacy of vanzacaftor–tezacaftor–deutivacaftor in adults with cystic fibrosis : randomised, double-blind, controlled, phase 2 trials ', The Lancet Respiratory Medicine, vol. 11, no. 6, pp. 550-562 . https://doi.org/10.1016/S2213-2600(22)00504-5
LANCET RESPIRATORY MEDICINE
Background: Elexacaftor–tezacaftor–ivacaftor has been shown to be safe and efficacious in people with cystic fibrosis and at least one F508del allele. Our aim was to identify a novel cystic fibrosis transmembrane conductance regulator (CFTR) modu
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::72b19fd4ef9823a3f92122d18b15dec4
https://research.vumc.nl/en/publications/0a8b171c-28b7-4da9-8e4a-5749733cacf9
https://research.vumc.nl/en/publications/0a8b171c-28b7-4da9-8e4a-5749733cacf9
Autor:
Jennifer L. Taylor-Cousar, Andreas Kaiser, François Vermeulen, Peter Sandner, Clare Saunders, Nico Derichs, Isabelle Fajac, Renee Jensen, Jane C. Davies, Steven M. Rowe, Anja Hoffmann, Damian G. Downey, Christine E. Bear, Karoline Droebner, Soundos Saleh, George M. Solomon, Felix Ratjen, Daniel B. Rosenbluth, Anne Malfroot, Elizabeth Tullis, Stefan Willmann, Dilip Nazareth
Publikováno v:
Rio-CF Study Group, Derichs, N, Taylor-Cousar, J L, Davies, J C, Fajac, I, Tullis, E, Nazareth, D, Downey, D G, Rosenbluth, D, Malfroot, A, Saunders, C, Jensen, R, Solomon, G M, Vermeulen, F, Kaiser, A, Willmann, S, Saleh, S, Droebner, K, Sandner, P, Bear, C E, Hoffmann, A, Ratjen, F & Rowe, S M 2021, ' Riociguat for the treatment of Phe508del homozygous adults with cystic fibrosis ', Journal of Cystic Fibrosis, vol. 20, no. 6, pp. 1018-1025 . https://doi.org/10.1016/j.jcf.2021.07.015
BACKGROUND: Riociguat is a first-in-class soluble guanylate cyclase stimulator for which preclinical data suggested improvements in cystic fibrosis transmembrane conductance regulator (CFTR) function. METHODS: This international, multicenter, two-par
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::a372e9b8ce7beb6e7e0a0ae4c60ecd2f
https://pure.qub.ac.uk/en/publications/0aba0b21-9b6d-4143-a70d-193cd26ffef8
https://pure.qub.ac.uk/en/publications/0aba0b21-9b6d-4143-a70d-193cd26ffef8
Autor:
Kathleen J. Ramos, E. Tallarico, Amy Lucy, Edward F. McKone, Sarah E. Hempstead, Patrick Smith, Daniel B. Rosenbluth, Albert Faro, Joseph M. Pilewski, Alice L. Gray, Jordan M. Dunitz
Publikováno v:
J Cyst Fibros
Objective Provide recommendations to the cystic fibrosis (CF) community to facilitate timely referral for lung transplantation for individuals with CF. Methods The CF Foundation organized a multidisciplinary committee to develop CF Lung Transplant Re
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::3a631f6c30abbaada920c4a71dd73b8c
https://doi.org/10.1016/j.jcf.2019.03.002
https://doi.org/10.1016/j.jcf.2019.03.002
Autor:
Amy Hoffman, Christopher H. Goss, Patricia Burks, David P. Nichols, John P. Clancy, George Z. Retsch-Bogart, Jill M. VanDalfsen, K. Pearson, Nicole Mayer-Hamblett, Daniel B. Rosenbluth
Publikováno v:
Journal of Cystic Fibrosis
Highlights • The Severe Acute Respiratory Syndrome Coronavirus (SARS-CoV-2) global pandemic has significantly impacted CF clinical research. • An electronic survey was sent to Therapeutic Development Network (TDN) sites to monitor the impact. •
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::322d6066d1efe5d9fbe359943a3e93f5
http://europepmc.org/articles/PMC7834129
http://europepmc.org/articles/PMC7834129
Autor:
Joanne Billings, Raksha Jain, Charlotte C. Teneback, Douglas Conrad, Daniel B. Rosenbluth, Barbara A. Bailey, Jonathan L. Koff
Publikováno v:
Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society. 20(1)
Background Cystic Fibrosis (CF) is a multi-systemic disorder resulting from genetic variation in the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) gene which can result in bronchiectasis, chronic sinusitis, pancreatic malabsorption, chol
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::6357dbb88774e4125a47323cfd8c0b53
https://pubmed.ncbi.nlm.nih.gov/32948498
https://pubmed.ncbi.nlm.nih.gov/32948498
Autor:
Patrick Smith, Jordan M. Dunitz, Edward F. McKone, Joseph M. Pilewski, Daniel B. Rosenbluth, Sarah E. Hempstead, Alice L. Gray, Amy Lucy, E. Tallarico, Kathleen J. Ramos, Albert Faro
Publikováno v:
The Journal of Heart and Lung Transplantation. 38:S332-S333
Purpose Nearly 40% of individuals with cystic fibrosis (CF) and decreased FEV1 die without lung transplantation (LTx) in the United States, with an annual mortality rate of 10%. In addition, a substantial proportion of CF individuals with rapidly dec
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::c268d2306a1deba185e7a0de7b8e02ec
https://doi.org/10.1016/j.healun.2019.01.840
https://doi.org/10.1016/j.healun.2019.01.840
Publikováno v:
Pediatric Pulmonology. 49:28-35
Background Epidemiologic data from studies of airway diseases, such as asthma, chronic obstructive pulmonary disease, and cystic fibrosis indicate a gender disparity where women have worse outcomes. The explanation for this is largely unknown. We hyp
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::96459ed7bc36f1aff81dba0c25dac8d8
https://doi.org/10.1002/ppul.22767
https://doi.org/10.1002/ppul.22767
Publikováno v:
Respiratory Care. 57:221-228
BACKGROUND: Conventional chest physical therapy (CCPT), applied by therapists using cupped hands to perform percussion, is commonly used in hospitalized adults. However, increased work load demands and occupational health concerns (eg, carpal tunnel
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::ac7356f47135c072ab7e0add52cc2d6c
https://doi.org/10.4187/respcare.01299
https://doi.org/10.4187/respcare.01299
Autor:
Jane L. Burns, Marcia Katz, Ronald L. Gibson, Julia Emerson, Moira L. Aitken, Wade W. Benton, Samuel M. Moskowitz, Douglas B. Hornick, Sharon McNamara, Patricia M. Joseph, Daniel B. Rosenbluth, David M. Orenstein, Richard Shell, Richard C. Ahrens
Publikováno v:
Pediatric Pulmonology. 46:184-192
Rationale In cystic fibrosis (CF), conventional antibiotic susceptibility results correlate poorly with clinical outcomes. We hypothesized that biofilm testing would more accurately reflect the susceptibilities of bacteria infecting CF airways. Metho
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::0626330569027df725fef82c8858dff6
https://doi.org/10.1002/ppul.21350
https://doi.org/10.1002/ppul.21350
Autor:
Christopher Short, S. Langer, Jennifer L. Taylor-Cousar, Dilip Nazareth, Daniel B. Rosenbluth, Renee Jensen, Nico Derichs, Soundos Saleh, Jane C. Davies, Stefan Willmann, François Vermeulen, Damian G. Downey, Clare Saunders, Anja Hoffmann, Isabelle Fajac, Elizabeth Tullis, Andreas Kaiser, Felix Ratjen, Steven M. Rowe, Anne Malfroot, George M. Solomon
Publikováno v:
Journal of Cystic Fibrosis. 17:S67
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::f981e69e02d562ec5965c225c0054d1a
https://doi.org/10.1016/s1569-1993(18)30325-4
https://doi.org/10.1016/s1569-1993(18)30325-4