Zobrazeno 1 - 10
of 12
pro vyhledávání: '"Anne Munck"'
Autor:
James C. Sullivan, Kris De Boeck, Paul A. Negulescu, Anne Munck, Meredith C. Fidler, Mark Higgins, Fredrick Van Goor, Sylvia F. Boj, Matteo Moretto Zita, Alexandra Buckley, Robert G.J. Vries, Marvin Statia
Publikováno v:
Clinical and Translational Science, Vol 14, Iss 2, Pp 656-663 (2021)
Clinical and Translational Science
Clinical and Translational Science
In previous work, participants with a G970R mutation in cystic fibrosis transmembrane conductance regulator (CFTR) (c.2908G>C) had numerically lower sweat chloride responses during ivacaftor treatment than participants with other CFTR gating mutation
Autor:
John Tsanakas, I. Asherova, Olga Bede, Melinda Solomon, Gerhild Angyalosi, Jutta Hammermann, Katalin Bolbás, Robert Maykut, Michael Fayon, Elena Chertok, Martha L McKinney, Nipa Alon, Ferenc Gonczi, Felix Ratjen, Vladimir Bulatov, Anne Munck, Carla Colombo, Essam Gouda, Alexander Moeller
Publikováno v:
Journal of Cystic Fibrosis. 18:78-85
Antibiotic eradication treatment is the standard-of-care for cystic fibrosis (CF) patients with early Pseudomonas aeruginosa (Pa)-infection; however, evidence from placebo-controlled trials is limited.This double-blind, placebo-controlled trial rando
Autor:
Pierre-Régis Burgel, Anne Munck, Isabelle Durieu, Raphaël Chiron, Laurent Mely, Anne Prevotat, Marlene Murris-Espin, Michele Porzio, Michel Abely, Philippe Reix, Christophe Marguet, Julie Macey, Isabelle Sermet-Gaudelus, Harriet Corvol, Stéphanie Bui, Lydie Lemonnier, Clémence Dehillotte, Jennifer Da Silva, Jean-Louis Paillasseur, Dominique Hubert, Julie Mounard, Claire Poulet, Cinthia Rames, Christine Person, Françoise Troussier, Thierry Urban, Marie-Laure Dalphin, Jean-Claude Dalphin, Didier Pernet, Bénédicte Richaud-Thiriez, Mickael Fayon, Julie Macey-Caro, Karine Campbell, Muriel Laurans, Corinne Borderon, Marie-Christine Heraud, André Labbé, Sylvie Montcouquiol, Laurence Bassinet, Natascha Remus, Annlyse Fanton, Anne Houzel-Charavel, Frédéric Huet, Stéphanie Perez-Martin, Amale Boldron-Ghaddar, Manuela Scalbert, Boubou Camara, Catherine Llerena, Isabelle Pin, Sébastien Quétant, Aurélie Cottereau, Antoine Deschildre, Alice Gicquello, Thierry Perez, Lidwine Stervinou-Wemeau, Caroline Thumerelle, Benoit Wallaert, Nathalie Wizla, Jane Languepin, Céline Ménétrey, Magalie Dupuy-Grasset, Lucie Bazus, Clelia Buchs, Virginie Jubin, Marie-Christine Werck-Gallois, Catherine Mainguy, Thomas Perrin, Agnès Toutain-Rigolet, Stéphane Durupt, Quitterie Reynaud, Raphaele Nove-Josserand, Melisande Baravalle-Einaudi, Bérangère Coltey, Nadine Dufeu, Jean-Christophe Dubus, Nathalie Stremler, Davide Caimmi, Yves Billon, Jocelyne Derelle, Sébastien Kieffer, Anne-Sophie Pichon, Cyril Schweitzer, Aurélie Tatopoulos, Sarah Abbes, Tiphaine Bihouée, Isabelle Danner-Boucher, Valérie David, Alain Haloun, Adrien Tissot, Sylvie Leroy, Carole Bailly-Piccini, Annick Clément, Aline Tamalet, Isabelle Honoré, Reem Kanaan, Clémence Martin, Cécile Bailly, Frédérique Chédevergne, Jacques De Blic, Brigitte Fauroux, Murielle Le Bourgeois, Bertrand Delaisi, Michèle Gérardin, Michel Abély, Bruno Ravoninjatovo, Chantal Belleguic, Benoit Desrues, Graziella Brinchault, Michel Dagorne, Eric Deneuville, Sylvaine Lefeuvre, Anne Dirou, Jean Le Bihan, Sophie Ramel, Stéphane Dominique, Annabelle Payet, Romain Kessler, Vincent Rosner, Laurence Weiss, Sandra de Miranda, Dominique Grenet, Abdoul Hamid, Clément Picard, François Brémont, Alain Didier, Géraldine Labouret, Marie Mittaine, Marlène Murris-Espin, Laurent Têtu, Laure Cosson, Charlotte Giraut, Anne-Cécile Henriet, Julie Mankikian, Sophie Marchand, Sandrine Hugé, Véronique Storni, Emmanuelle Coirier-Duet
Publikováno v:
American Journal of Respiratory and Critical Care Medicine
American Journal of Respiratory and Critical Care Medicine, American Thoracic Society, 2020, 201 (2), pp.188-197. ⟨10.1164/rccm.201906-1227OC⟩
American Journal of Respiratory and Critical Care Medicine, 2020, 201 (2), pp.188-197. ⟨10.1164/rccm.201906-1227OC⟩
American Journal of Respiratory and Critical Care Medicine, American Thoracic Society, 2020, 201 (2), pp.188-197. ⟨10.1164/rccm.201906-1227OC⟩
American Journal of Respiratory and Critical Care Medicine, 2020, 201 (2), pp.188-197. ⟨10.1164/rccm.201906-1227OC⟩
International audience; Rationale: Lumacaftor-ivacaftor is a CFTR (cystic fibrosis transmembrane conductance regulator) modulator combination recently approved for patients with cystic fibrosis (CF) homozygous for the Phe508del mutation.Objectives: T
Autor:
Sarah Jane Schwarzenberg, Barry Lubarsky, Frank A J A Bodewes, Daniel Gelfond, Drucy Borowitz, Anne Munck, Michael Wilschanski
Publikováno v:
Digestive Diseases and Sciences, 61(1), 198-207. SPRINGER
The cystic fibrosis (CF) transmembrane conductance regulator (CFTR) gating mutation G551D prevents sufficient ion transport due to reduced channel-open probability. Ivacaftor, an oral CFTR potentiator, increases the channel-open probability.To furthe
Inhaled dry powder mannitol in children with cystic fibrosis: A randomised efficacy and safety trial
Autor:
Alexander Moeller, Anne Munck, Brett Charlton, S. Volpi, Joachim Riethmüller, Harm A.W.M. Tiddens, Eric G. Haarman, Anne Malfroot, J. Leadbetter, Larry C. Lands, K. De Boeck, J. Hull
Publikováno v:
Journal of Cystic Fibrosis, 16(3), 380-387. Elsevier
for the DPM-CF-204 Study Group 2017, ' Inhaled dry powder mannitol in children with cystic fibrosis : A randomised efficacy and safety trial ', Journal of Cystic Fibrosis, vol. 16, no. 3, pp. 380-387 . https://doi.org/10.1016/j.jcf.2017.02.003
for the DPM-CF-204 Study Group 2017, ' Inhaled dry powder mannitol in children with cystic fibrosis : A randomised efficacy and safety trial ', Journal of Cystic Fibrosis, vol. 16, no. 3, pp. 380-387 . https://doi.org/10.1016/j.jcf.2017.02.003
Introduction Inhaled mannitol has beneficial effects on lung function, mucociliary clearance, quality of life and sputum properties. This trial examined the efficacy of inhaled mannitol in children with cystic fibrosis (CF). Methods The efficacy of i
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::2272d853fb64d56bc4600e99b062765b
https://pure.eur.nl/en/publications/156ffc86-1a6f-4029-be1b-f50a747a3972
https://pure.eur.nl/en/publications/156ffc86-1a6f-4029-be1b-f50a747a3972
Autor:
Rosaria Casciaro, Philippe Reix, Adria Perez-Rovira, M. H. Smet, Desmond Cox, Anne Mehl, Pilar Garcia Peña, Torkel B. Brismar, Annmarie Jeanes, G Lucigrai, Silvia Gartner, Veronika Skalická, Marleen de Bruijne, Jacqueline Payen De La Garanderie, Marco Di Maurizio, Lena Hjelte, Marianne Nuijsink, I. Sermet, Kris De Boeck, David Rea, Mariëtte van de Corput, Herma C. Holscher, Cesare Braggion, Marcel van Straten, Harm A.W.M. Tiddens, Laureline Berteloot, Wieying Kuo, Jane C. Davies, David M. Hansell, C. Kors van der Ent, Pim A. de Jong, Nanko de Graaf, Ahmed Kheniche, Anne Munck, Isabelle Fajac, Tim W.R. Lee, Hana Vitouskova, Florian Streitparth
Publikováno v:
European Respiratory Journal, 47(6), 1706. European Respiratory Society
Progressive cystic fibrosis (CF) lung disease is the main cause of mortality in CF patients. CF lung disease starts in early childhood. With current standards of care, respiratory function remains largely normal in children and more sensitive outcome
Autor:
M. Lebourgeois, Catherine C. Ajzenman, Jean Navarro, Anne Munck, Yves Aigrain, M. Gerardin, Corinne Alberti
Publikováno v:
Journal of Pediatric Surgery. 41:1556-1560
Objective This matched case-control study compared the nutritional and the pulmonary long-term outcomes of cystic fibrosis (CF) patients presenting a history of meconium ileus (MI) with early-diagnosed symptomatic CF without MI (non-MI). Material and
Autor:
Anne Munck, Hermine Laselve, Panayotis Lykavieris, Dominique Debray, Bertrand Dousset, Anne Sardet, Frédéric Gauthier, Olivier Bernard
Publikováno v:
Journal of Hepatology. 31:77-83
Background/Aim: Variceal bleeding is the most severe complication in patients with cystic fibrosis-associated liver cirrhosis, who often do not have severe respiratory failure. The advent of liver transplantation has broadened the treatment options.
Autor:
Michelle S. Howenstine, Gerard J. Canny, Jochen G. Mainz, Claire E. Wainwright, Mark A. Chilvers, Anne Munck, Haihong Li, Karl Yen, Richard C. Ahrens, Jane C. Davies, Claudia L. Ordoñez, Sally Rodriguez
Publikováno v:
American journal of respiratory and critical care medicine. 187(11)
Ivacaftor (VX-770), a cystic fibrosis transmembrane conductance regulator (CFTR) potentiator, has been shown to improve lung function, pulmonary exacerbation rate, respiratory symptoms, and weight gain compared with placebo in patients with cystic fi
Publikováno v:
Thorax. 65(4)
Rationale: Antibiotic therapy for early Pseudomonas aeruginosa infection in patients with cystic fibrosis (CF) is effective, but the optimal therapeutic regimen and duration for early treatment remains unclear. The EarLy Inhaled Tobramycin for Eradic