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of 10
pro vyhledávání: '"Simon R. Johnson"'
Autor:
Debbie Clements, Suzanne Miller, Roya Babaei-Jadidi, Mike Adam, S. Steven Potter, Simon R. Johnson
Publikováno v:
American Journal of Physiology-Lung Cellular and Molecular Physiology. 322:L283-L293
Lymphangioleiomyomatosis (LAM) is a female-specific cystic lung disease in which tuberous sclerosis complex 2 (TSC2)-deficient LAM cells, LAM-associated fibroblasts (LAFs), and other cell types infiltrate the lungs. LAM lesions can be associated with
Autor:
Roya Babaei-Jadidi, Marcos Castellanos Uribe, Suzanne Miller, Peter Bradding, Abdolrahman S. Nateri, Iain D Stewart, Debbie Clements, Zoe M Thompson, Sean T. May, Arundhati Dongre, Simon R. Johnson
Publikováno v:
American Journal of Respiratory and Critical Care Medicine
Rationale: Lymphangioleiomyomatosis (LAM) is a multisystem disease that causes lung cysts and respiratory failure. Loss of TSC (tuberous sclerosis complex) gene function results in a clone of “LAM ...
Publikováno v:
The Lancet. Respiratory medicine. 9(11)
Lymphangioleiomyomatosis (LAM) is a slowly progressive, low-grade, metastasising neoplasm of women, characterised by infiltration of the lung parenchyma with abnormal smooth muscle-like cells, resulting in cystic lung destruction. The invading cell i
Funder: Nottingham Molecular Pathology Node
Funder: NIHR Rare Diseases Translational Research Collaboration
Background: Lymphangioleiomyomatosis (LAM) is a rare multisystem disease almost exclusively affecting women which causes loss of lun
Funder: NIHR Rare Diseases Translational Research Collaboration
Background: Lymphangioleiomyomatosis (LAM) is a rare multisystem disease almost exclusively affecting women which causes loss of lun
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::7c57dddbac3e27fe082cd5760992f137
https://www.repository.cam.ac.uk/handle/1810/306638
https://www.repository.cam.ac.uk/handle/1810/306638
Autor:
Kevin K. Brown, Yoshikazu Inoue, Karen Smith, Kevin C. Wilson, Angelo M. Taveira-Da Silva, Steven A. Sahn, Gregory P. Downey, Simon R. Johnson, Vincent Cottin, Kuniaki Seyama, Nishant Gupta, MeiLan K. Han, Jeffrey T. Chapman, Eugene J. Sullivan, Jan Brozek, Lisa R. Young, Elizabeth P. Henske, Jeanine D'Armiento, Joel Moss, Geraldine R. Finlay, John J. Bissler, Cristopher A. Meyer, Francis X. McCormack, Robert M. Kotloff, Wendy K. Steagall, Thomas V. Colby, Jay H. Ryu, Charlie Strange, Jean F. Cordier, Kathryn A. Wikenheiser-Brokamp, Brent W. Kinder, Connie G. Glasgow
Background: Lymphangioleiomyomatosis (LAM) is a rare cystic lung disease that primarily affects women. The purpose of these guidelines is to provide recommendations for the diagnosis and treatment of LAM.Methods: Systematic reviews were performed to
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::3747eb67c592ce58b0178884bf638418
https://europepmc.org/articles/PMC5803656/
https://europepmc.org/articles/PMC5803656/
Publikováno v:
Respiratory Medicine. 103(5):766-772
SummaryLymphangioleiomyomatosis (LAM) is a rare lung disease affecting women. Following case reports that pregnancy exacerbates LAM, patients are frequently advised to avoid pregnancy. Our objective was to determine pregnancy and health outcomes in L
Publikováno v:
Thorax. 70(12)
Lymphangioleiomyomatosis (LAM) is a rare multisystem disease. Progressive airflow limitation, pneumothorax and angiomyolipoma-related bleeding are major morbidities. As treatments are available for these complications, we prospectively audited loss o
Publikováno v:
Thorax. 60:875-879
To provide a comprehensive update of the clinical picture of lymphangioleiomyomatosis (LAM) using two large patient registries.A cross sectional questionnaire survey which included questions on 14 LAM symptoms, pneumothorax, tuberous sclerosis comple
Background: Lymphangioleiomyomatosis (LAM), a rare disease affecting women, is caused by somatic mutations in the tuberous sclerosis complex genes. Methods: A case–control questionnaire study was carried out examining parental and family history, p
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::f2bc55494d6f6278382e96b5a73a3755
https://europepmc.org/articles/PMC1746512/
https://europepmc.org/articles/PMC1746512/
Publikováno v:
Thorax. 67:A49.2-A49
Background Lymphangioleiomyomatosis (LAM) is a rare disease of women categorised by lung cysts, lymphatic abnormalities and angiomyolipomas; a benign tumour occurring chiefly in the kidneys. Although benign, the tumours can enlarge causing symptoms a