Zobrazeno 1 - 10
of 130
pro vyhledávání: '"Werner Stenzel"'
Autor:
Werner Stenzel, Corinna Preuße, Elise Siegert, Katrin Hahn, Felix Kleefeld, Jan Zoske, Udo Schneider
Publikováno v:
Neurological Research and Practice, Vol 3, Iss 1, Pp 1-9 (2021)
Neurological Research and Practice
Neurological Research and Practice
Background There have been numerous classification systems to diagnose corresponding myositis subtypes and select appropriate therapeutic measures. However, the lack of a broad consensus on diagnostic criteria has led to clinical uncertainties. The o
Publikováno v:
Neuromuscular Disorders. 31:1051-1061
Myositis in childhood can occur under different conditions and with various aetiologies, juvenile dermatomyositis (jDM) being by far the most frequent entity. The exact diagnostic workup and precise assessment of muscular as well as extramuscular inv
Publikováno v:
Aktuelle Rheumatologie. 46:343-360
ZusammenfassungDie idiopathischen inflammatorischen Myopathien (IIM) sind eine Gruppe entzündlicher Muskelerkrankungen für deren Diagnosestellung, Verlaufsbeurteilung, Prognoseabschätzung und Risikostratifizierung Biomarker eine jeweils essentiell
Publikováno v:
Zeitschrift für Rheumatologie. 80:884-888
ZusammenfassungWir schildern den Fall einer 73-jährigen Patientin mit malignem Melanom, die eine rasch progrediente Dermatosklerose der Arme und Beine sowie Myalgien und Beugekontrakturen unter der Therapie mit dem Immuncheckpoint-Inhibitor Nivoluma
Autor:
Corinna Preuße, Carsten Dittmayer, Werner Stenzel, Elise Siegert, Jakob Höppner, Vincent Casteleyn, Hans-Hilmar Goebel, Udo Schneider, Rieke Alten, Gerd R Burmester, Felix Kleefeld, Akinori Uruha, Kathrin Hahn
Publikováno v:
Acta Neuropathologica. 141:917-927
Systemic sclerosis represents a chronic connective tissue disease featuring fibrosis, vasculopathy and autoimmunity, affecting skin, multiple internal organs, and skeletal muscles. The vasculopathy is considered obliterative, but its pathogenesis is
Autor:
Sarah Guégan, Nathalie Costedoat-Chalumeau, Vincent Descamps, Emmanuel Bergot, G. Monseau, Yoland Schoindre, C. Martel, Stéphane Barete, Cristian Bulai Livideanu, Valérie Jooste, Aude Rigolet, Achille Aouba, Thierry Zenone, Hubert de Boysson, Emmanuelle Salort-Campana, Jean-Emmanuel Kahn, Sarah Leonard-Louis, Werner Stenzel, Baptiste Hervier, Sylvain Audia, Antoine Dossier, Nicolas Schleinitz, Eric Hachulla, Alain Meyer, Laurent Mortier, Marie Lacoste, Guillaume Moulis, Serge Madaule, Florian Perez, Kuberaka Mariampillai, Anne-Marie Bouvier, Yves Allenbach, Laurence Verneuil, Benjamin Terrier, Nicolas Champtiaux, Thomas Papo, Séverine Genot, Maxime Samson, Agathe Masseau, Thierry Maisonobe, Marie-Aleth Richard, Olivier Benveniste, Boris Bienvenu, François Maurier, Guillaume Lefèvre, Anne-Marie Piette, O. Landon-Cardinal
Publikováno v:
Journal of the American Academy of Dermatology. 83:1759-1763
Autor:
Gerd-Rüdiger Burmester, Jan-Paul Frese, Maximilian Dölling, Udo Schneider, Christian Furth, Markus Herbert Lerchbaumer, Malte C Kleinschmidt, Robert Biesen, Werner Stenzel, Désirée Schaumburg
Publikováno v:
Rheumatology. 60:e432-e434
Publikováno v:
Current Opinion in Neurology. 33:590-603
Purpose of review Discoveries of myositis-specific antibodies, transcriptomic signatures, and clinicoseropathological correlation support classification of idiopathic inflammatory myopathies (IIM) into four major subgroups: dermatomyositis, immune-me
Autor:
Andreas Meisel, Markus Schuelke, Jens-Carsten Rückert, Sarah Hoffmann, Lutz Harms, Werner Stenzel, Hans-Hilmar Goebel
Publikováno v:
Acta Neuropathologica
Autor:
Anna Tietze, Angela M. Kaindl, Werner Stenzel, Marc Nikolaus, Markus Schuelke, Leonille Schweizer, Ellen Knierim
Publikováno v:
Brain and Development. 41:901-904
MELAS-syndrome (mitochondrial myopathy, encephalomyopathy, lactic acidosis, and stroke-like episodes) is a multisystem disorder with various presentations. Common clinical manifestations include stroke-like episodes, encephalopathy with seizures, mus