Zobrazeno 1 - 10
of 30
pro vyhledávání: '"Mitsuyoshi Suzuki"'
Autor:
Hiroyuki Kusuhara, Mitsuyoshi Suzuki, Yoshiki Miura, Shuhei Osaka, Yusuke Sabu, Hisamitsu Hayashi, Ayumu Mizutani, Satoshi Nakano, Kei Minowa, Yuka Hiraoka, Tadahaya Mizuno, Saeko Hirai, Toshiaki Shimizu
Publikováno v:
Molecular Genetics and Metabolism. 132:220-226
Urea cycle disorders (UCDs), inborn errors of hepatocyte metabolism, result in the systemic accumulation of ammonia to toxic levels. Sodium 4-phenylbutyrate (NaPB), a standard therapy for UCDs for over 20 years, generates an alternative pathway of ni
Publikováno v:
Pediatrics International. 63:137-149
Acute recurrent pancreatitis (ARP) is defined as two distinct episodes of acute pancreatitis (AP), whereas chronic pancreatitis (CP) is caused by persistent inflammation of the pancreas. In children they are caused by genetic mutations, autoimmune pa
Autor:
Nobuo Yoshiike, Shinobu Ida, Toshihiro Ohura, Akihide Sugiyama, Kazue Kawakami, Daisuke Tanaka, Yuko Bito, Chiharu Tsutsumi, Akihisa Okumura, Katsumi Mizuno, Sotaro Mushiake, Toru Kikuchi, Mitsuyoshi Suzuki, Yoshio Hanawa, Kimitaka Takitani, Kazuo Okada, Motoichiro Sakurai, Masanobu Kawai, Mikako Inokuchi, Hiroko Kodama, Mitsuhiko Hara, Hiroaki Inomata, Tatsuya Oguni, Setsuko Ito, Shigetaka Sugihara, Keiichi Uchida, Toshiaki Shimizu
Publikováno v:
Pediatrics International
For preterm and very low birthweight infants, the mother’s own milk is the best nutrition. Based on the latest information for mothers who give birth to preterm and very low birthweight infants, medical staff should encourage and assist mothers to
Publikováno v:
Journal of Pediatric Endocrinology and Metabolism. 32:1395-1398
Background Cholesterol metabolism has dramatically changed under hyperthyroid status. However, a combination of hyperthyroidism and cholecystolithiasis is very rare. Case presentation We report a case of cholelithiasis accompanied by hyperthyroidism
Autor:
Mitsuyoshi Suzuki, Yuko Sakamoto, Satoshi Nakano, Akifumi Tokita, Masahiko Nozawa, Muneaki Ishijima, Lizu Liu, Sung-Gon Kim, Kazuo Kaneko, Toshiaki Shimizu
Publikováno v:
Calcified Tissue International. 106:95-103
When children around 2-year-old show leg bowing without lower-limb radiographic abnormalities for rickets, the leg bowing is classified as “physiologic” genu varum without conducting a blood test. However, it has recently been suggested that todd
Autor:
Rebecca K. Martin, Mitsuyoshi Suzuki, Sandra A. LaSalle, Daniel Rodriguez-Agudo, Phillip B. Hylemon, Dalila Marques, Michael Fuchs, Hiroshi Nittono, Genta Kakiyama, Tsuyoshi Murai, William M. Pandak, Hajime Takei, Taishi Hashiguchi, Gregorio Gil, Huiping Zhou, Richard M. Green, Sandra K. Erickson, Xiaoying Liu
Publikováno v:
J Lipid Res
Journal of Lipid Research, Vol 61, Iss 12, Pp 1629-1644 (2020)
Journal of Lipid Research, Vol 61, Iss 12, Pp 1629-1644 (2020)
NAFLD is an important public health issue closely associated with the pervasive epidemics of diabetes and obesity. Yet, despite NAFLD being among the most common of chronic liver diseases, the biological factors responsible for its transition from be
Autor:
Hiroshi Nittono, Takao Kurosawa, Keiko Sato, Genta Kakiyama, Mitsuyoshi Suzuki, Hiroaki Sato, Akihiko Kimura, Toshiaki Shimizu, Hajime Takei, William M. Pandak, Tsuyoshi Murai, Nakayuki Naritaka
Publikováno v:
Steroids. 164
Bile acid compositions are known to change dramatically after birth with aging. However, no reports have described the transition of conjugated urinary bile acids from the neonatal period to adulthood, and such findings would noninvasively offer insi
Autor:
Masayoshi Kage, Yasuhiro Hasegawa, Takako Yoshioka, Kazuhiko Bessho, Ken Tanikawa, Takashi Ishige, Ayano Inui, Atsuko Nakazawa, Yoh Zen, Hisamitsu Hayashi, Mureo Kasahara, Kazuo Imagawa, Hiroki Kondou, Mitsuyoshi Suzuki, Kouji Yamamoto
Publikováno v:
Hepatology research : the official journal of the Japan Society of HepatologyReferences. 50(6)
Aim Bile salt export pump (BSEP) deficiency manifests a form of progressive intrahepatic cholestasis. This study aimed to establish a scoring system of liver histology for the uncommon genetic condition. Methods After a roundtable discussion and hist
Autor:
Kazuhiko Bessho, Hiroyuki Kusuhara, Atsuko Nakazawa, Hironori Kusano, Ayano Inui, Saeko Hirai, Satoshi Nakano, Hisamitsu Hayashi, Kei Minowa, Satoshi Watanabe, Masayoshi Kage, Yusuke Sabu, Yoh Zen, Yoshihiro Azuma, Toshiaki Shimizu, Shuhei Osaka, Hiroki Kondou, Ken Tanikawa, Hidefumi Nakamura, Takeshi Kimura, Mitsuyoshi Suzuki
Publikováno v:
Scientific Reports
Scientific Reports, Vol 9, Iss 1, Pp 1-12 (2019)
Scientific Reports, Vol 9, Iss 1, Pp 1-12 (2019)
Progressive familial intrahepatic cholestasis (PFIC), a rare inherited disorder, progresses to liver failure in childhood. We have shown that sodium 4-phenylbutyrate (NaPB), a drug approved for urea cycle disorders (UCDs), has beneficial effects in P
Autor:
Hironori Nagasaka, Ayano Inui, Satoshi Watanabe, Akinari Fukuda, Yasuhiro Hasegawa, Hisamitsu Hayashi, Kei Minowa, Takao Togawa, Hiroyuki Kusuhara, Hiroki Kondou, Koji Muroya, Kazuhiko Bessho, Sotaro Naoi, Mika Sasaki, Yu Hirose, Mureo Kasahara, Daiki Abukawa, Satoshi Nakano, Mitsuyoshi Suzuki
Publikováno v:
EBioMedicine
EBioMedicine, Vol 27, Iss C, Pp 187-199 (2018)
EBioMedicine, Vol 27, Iss C, Pp 187-199 (2018)
Progressive familial intrahepatic cholestasis type 1 (PFIC1), a rare inherited recessive disease resulting from a genetic deficiency in ATP8B1, progresses to liver failure. Because of the difficulty of discriminating PFIC1 from other subtypes of PFIC