Zobrazeno 1 - 10
of 15
pro vyhledávání: '"Dumitru Moldovan"'
Autor:
Dumitru Moldovan, Katalin Csép, Noémi Bara, Daniela Dobru, Enikő Mihály, Adina Hutanu, Valentin Nădășan, Gabriella Gábos
Publikováno v:
Romanian Journal of Laboratory Medicine, Vol 27, Iss 3, Pp 255-267 (2019)
Background: Hereditary angioedema due to C1 inhibitor deficiency (C1-INH-HAE) caused by SERPING1 mutations is a rare monogenic disorder characterized by a high frequency of de novo mutations, allelic heterogeneity and populational differences. Geno-
Autor:
Vesna Grivcheva-Panovska, Markus Magerl, Henriette Farkas, Avner Reshef, Stephen Fritz, Dumitru Moldovan, Bruno Giannetti, Aharon Kessel, Vaclava Gutova, Anurag Relan, Shmuel Kivity, Maria Klimaszewska-Rembiasz
Publikováno v:
Pediatric Allergy and Immunology
Background Attacks of hereditary angioedema (HAE) due to C1 esterase inhibitor deficiency (C1‐INH‐HAE) usually begin during childhood or adolescence. However, limited data are available regarding indications and modalities of treatment of childre
Autor:
Jennifer Schranz, Jim Christensen, Kraig W. Jacobson, Emel Aygören-Pürsün, Inmaculada Martinez-Saguer, Yongqiang Tang, D. Soteres, Arthur Van Leerberghe, Moshe Y. Vardi, Peng Lu, Dumitru Moldovan, Sandra A. Nieto-Martinez
Publikováno v:
Pediatric Allergy and Immunology
Background Patients with hereditary angioedema with C1 inhibitor deficiency or dysfunction have burdensome recurrent angioedema attacks. The safety, efficacy, and health-related quality of life (HRQoL) outcomes of C1 inhibitor (C1-INH) prophylaxis (i
Autor:
Bruno Giannetti, Anurag Relan, Dumitru Moldovan, Sladjana Andrejevic, Shmuel Kivity, Marc A. Riedl, James R. Baker, Marco Cicardi, Avner Reshef, Roman Hakl, Richard F. Lockey, Joseph R. Harper, William H. Yang, Vesna Grivcheva-Panovska
Publikováno v:
The Lancet. 390:1595-1602
Summary Background Hereditary angio-oedema is a recurrent, oedematous disorder caused by deficiency of functional C1 inhibitor. Infusions of plasma-derived C1 esterase inhibitor deter attacks of hereditary angio-oedema, but the prophylactic effect of
Autor:
Inmaculada Martinez-Saguer, James Hao, Jim Christensen, D. Soteres, Dumitru Moldovan, Arthur Van Leerberghe, Jennifer Schranz, Emel Aygören-Pürsün, Kraig W Jacobson
Publikováno v:
International Archives of Allergy and Immunology. 173:114-119
Background: Hereditary angioedema (HAE) is a rare genetic disease causing unpredictable and potentially life-threatening subcutaneous and submucosal edematous attacks. Cinryze® (Shire ViroPharma Inc., Lexington, MA, USA), a nanofiltered C1 inhibitor
Publikováno v:
Journal of Interdisciplinary Medicine, Vol 1, Iss 3, Pp 287-292 (2016)
Hereditary angioedema (HAE) caused by a deficiency of C1 esterase inhibitor enzyme (C1-INH) is a very rare, autosomal dominantly inherited genetic disorder, characterized by recurrent peripheral angioedema, painful abdominal attacks and episodes of l
Autor:
Mikhail Rojavin, Dumitru Moldovan, Debora Williams-Herman, Krystyna Obtułowicz, Henrike Feuersenger, Jonathan M. Edelman, Todor Shirov, Thomas Machnig, Henriette Farkas, Lilian Varga
Publikováno v:
Annals of Allergy, Asthma & Immunology. 117:508-513
Background Limited data are available regarding C1 inhibitor (C1-INH) administration and anti–C1-INH antibodies. Objective To assess the incidence of antibody formation during treatment with pasteurized, nanofiltered plasma-derived C1-INH (pnfC1-IN
Safety of recombinant human C1 esterase inhibitor for hereditary angioedema attacks during pregnancy
Autor:
Dumitru Moldovan, Roman Hakl, Anurag Relan, William R. Lumry, Kimberly Poarch, Jonathan A. Bernstein, Grzegorz Porebski
Hereditary angioedema (HAE) is a rare (
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::ea878cf3b651375691ae3362483d42fe
https://ruj.uj.edu.pl/xmlui/handle/item/255949
https://ruj.uj.edu.pl/xmlui/handle/item/255949
Publikováno v:
Case Reports in Emergency Medicine
Case Reports in Emergency Medicine, Vol 2018 (2018)
Case Reports in Emergency Medicine, Vol 2018 (2018)
Emergency department (ED) physicians frequently encounter patients presenting with angioedema. Most of these involve histamine-mediated angioedema; however, less common forms of angioedema (bradykinin-mediated) also occur. It is vital physicians corr
Autor:
I. J. Ansotegui, Bruce L. Zuraw, Stephen Betschel, Marcus Maurer, Alexander Nast, Paul Potter, Marc A. Riedl, Inmaculada Martinez-Saguer, Mario Sánchez-Borges, Henriette Farkas, Ruby Pawankar, Emel Aygören-Pürsün, Bruce Ritchie, Constance H. Katelaris, Hilary Longhurst, Lanny J. Rosenwasser, W. R. Lumry, Timothy J. Craig, R. Lockey, Markus Magerl, Yuxiang Zhi, Michihiro Hide, Dumitru Moldovan, Tom Bowen, Konrad Bork, H. Balle Boysen, Anete Sevciovic Grumach
Publikováno v:
World Allergy Organization Journal
Hereditary Angioedema (HAE) is a rare and disabling disease. Early diagnosis and appropriate therapy are essential. This update and revision of the global guideline for HAE provides up-to-date consensus recommendations for the management of HAE. In t
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::57386d1ba42ac4a5f55b4701075ace83