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Autor:
Scott W. Canna, Jessie L. Barnum, Darshit Thakrar, Corinne Schneider, Julia Segal, Steven William Allen, Miguel Reyes-Múgica, Jessica D Daley, Cláudia M. Salgado, Serter Gumus
Publikováno v:
J Clin Immunol
Familial hemophagocytic lymphohistiocytosis (HLH) is a life-threatening hyperinflammatory syndrome resulting from defective cytotoxicity. A previously healthy 3-month-old female presented with fever, irritability, abdominal distention, and tachypnea.